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1. Mercer, JFB
   The molecular basis of copper-transport diseases
   TRENDS IN MOLECULAR MEDICINE
   
   J.F.B. Mercer, "The molecular basis of copper-transport diseases", TRENDS MO M, 7(2), 2001, pp. 64-69
2. Linder, MC
   Copper and genomic stability in mammals
   MUTATION RESEARCH-FUNDAMENTAL AND MOLECULAR MECHANISMS OF MUTAGENESIS
   
   M.C. Linder, "Copper and genomic stability in mammals", MUT RES-F M, 475(1-2), 2001, pp. 141-152
3. Hahn, S; Cho, K; Ryu, K; Kim, J; Pai, K; Kim, M; Park, H; Yoo, O
   Identification of four novel mutations in classical menkes disease and successful prenatal DNA diagnosis
   MOLECULAR GENETICS AND METABOLISM
   
   S. Hahn et al., "Identification of four novel mutations in classical menkes disease and successful prenatal DNA diagnosis", MOL GEN MET, 73(1), 2001, pp. 86-90
4. George, DH; Casey, RE
   Menkes disease after copper histidine replacement therapy: Case report
   PEDIATRIC AND DEVELOPMENTAL PATHOLOGY
   
   D.H. George e R.E. Casey, "Menkes disease after copper histidine replacement therapy: Case report", PEDIATR D P, 4(3), 2001, pp. 281-288
5. Nicolis, I; Deschamps, P; Curis, E; Corriol, O; Acar, V; Zerrouk, N; Chaumeil, JC; Guyon, F; Benazeth, S
   XAS applied to pharmaceuticals: drug administration and bioavailability
   JOURNAL OF SYNCHROTRON RADIATION
   
   I. Nicolis et al., "XAS applied to pharmaceuticals: drug administration and bioavailability", J SYNCHROTR, 8, 2001, pp. 984-986
6. Brewer, GJ
   Commentary: Landmark articles on copper in the field of human health
   JOURNAL OF TRACE ELEMENTS IN EXPERIMENTAL MEDICINE
   
   G.J. Brewer, "Commentary: Landmark articles on copper in the field of human health", J TR EL EXP, 14(2), 2001, pp. 191-194
7. Palmer, CA; Percy, AK
   Neuropathology of occipital horn syndrome
   JOURNAL OF CHILD NEUROLOGY
   
   C.A. Palmer e A.K. Percy, "Neuropathology of occipital horn syndrome", J CHILD NEU, 16(10), 2001, pp. 764-766
8. Strausak, D; Mercer, JFB; Dieter, HH; Stremmel, W; Multhaup, G
   Copper in disorders with neurological symptoms: Alzheimer's, Menkes, and Wilson diseases
   BRAIN RESEARCH BULLETIN
   
   D. Strausak et al., "Copper in disorders with neurological symptoms: Alzheimer's, Menkes, and Wilson diseases", BRAIN RES B, 55(2), 2001, pp. 175-185
9. van Mil, SWC; Klomp, LWJ; Bull, LN; Houwen, RHJ
   FIC1 disease: A spectrum of intrahepatic cholestatic disorders
   SEMINARS IN LIVER DISEASE
   
   S.W.C. van Mil et al., "FIC1 disease: A spectrum of intrahepatic cholestatic disorders", SEM LIV DIS, 21(4), 2001, pp. 535-544
10. Hansel, DE; May, V; Eipper, BA; Ronnett, GV
    Pituitary adenylyl cyclase-activating peptides and alpha-amidation in olfactory neurogenesis and neuronal survival in vitro
    JOURNAL OF NEUROSCIENCE
    
    D.E. Hansel et al., "Pituitary adenylyl cyclase-activating peptides and alpha-amidation in olfactory neurogenesis and neuronal survival in vitro", J NEUROSC, 21(13), 2001, pp. 4625-4636
11. Rolfs, A; Hediger, MA
    Intestinal metal ion absorption: an update
    CURRENT OPINION IN GASTROENTEROLOGY
    
    A. Rolfs e M.A. Hediger, "Intestinal metal ion absorption: an update", CURR OPIN G, 17(2), 2001, pp. 177-183
12. Riordan, SM; Williams, R
    The Wilson's disease gene and phenotypic diversity
    JOURNAL OF HEPATOLOGY
    
    S.M. Riordan e R. Williams, "The Wilson's disease gene and phenotypic diversity", J HEPATOL, 34(1), 2001, pp. 165-171
13. Gu, YH; Kodama, H; Murata, Y; Mochizuki, D; Yanagawa, Y; Ushijima, H; Shiba, T; Lee, CC
    ATP7A gene mutations in 16 patients with Menkes disease and a patient withoccipital horn syndrome
    AMERICAN JOURNAL OF MEDICAL GENETICS
    
    Y.H. Gu et al., "ATP7A gene mutations in 16 patients with Menkes disease and a patient withoccipital horn syndrome", AM J MED G, 99(3), 2001, pp. 217-222
14. Huffman, DL; O'Halloran, TV
    Function, structure, and mechanism of intracellular copper trafficking proteins
    ANNUAL REVIEW OF BIOCHEMISTRY
    
    D.L. Huffman e T.V. O'Halloran, "Function, structure, and mechanism of intracellular copper trafficking proteins", ANN R BIOCH, 70, 2001, pp. 677-701
15. Bekiesinska-Figatowska, M; Rokicki, D; Walecki, J; Gremida, M
    Menkes' disease with a Dandy-Walker variant: case report
    NEURORADIOLOGY
    
    M. Bekiesinska-Figatowska et al., "Menkes' disease with a Dandy-Walker variant: case report", NEURORADIOL, 43(11), 2001, pp. 948-950
16. Andrews, NC
    Mining copper transport genes
    PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA
    
    N.C. Andrews, "Mining copper transport genes", P NAS US, 98(12), 2001, pp. 6543-6545
17. Kuo, YM; Zhou, B; Cosco, D; Gitschier, J
    The copper transporter CTR1 provides an essential function in mammalian embryonic development
    PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA
    
    Y.M. Kuo et al., "The copper transporter CTR1 provides an essential function in mammalian embryonic development", P NAS US, 98(12), 2001, pp. 6836-6841
18. Narayanan, VS; Fitch, CA; Levenson, CW
    Tumor suppressor protein p53 mRNA and subcellular localization are alteredby changes in cellular copper in human Hep G2 cells
    JOURNAL OF NUTRITION
    
    V.S. Narayanan et al., "Tumor suppressor protein p53 mRNA and subcellular localization are alteredby changes in cellular copper in human Hep G2 cells", J NUTR, 131(5), 2001, pp. 1427-1432
19. Jordan, IK; Natale, DA; Koonin, EV; Galperin, MY
    Independent evolution of heavy metal-associated domains in copper chaperones and copper-transporting ATPases
    JOURNAL OF MOLECULAR EVOLUTION
    
    I.K. Jordan et al., "Independent evolution of heavy metal-associated domains in copper chaperones and copper-transporting ATPases", J MOL EVOL, 53(6), 2001, pp. 622-633
20. Hou, ZJ; Narindrasorasak, S; Bhushan, B; Sarkar, B; Mitra, B
    Functional analysis of chimeric proteins of the Wilson Cu(I)-ATPase (ATP7B) and ZntA, a Pb(II)/Zn(II)/Cd(II)-ATPase from Escherichia coli
    JOURNAL OF BIOLOGICAL CHEMISTRY
    
    Z.J. Hou et al., "Functional analysis of chimeric proteins of the Wilson Cu(I)-ATPase (ATP7B) and ZntA, a Pb(II)/Zn(II)/Cd(II)-ATPase from Escherichia coli", J BIOL CHEM, 276(44), 2001, pp. 40858-40863
21. Arnesano, F; Banci, L; Bertini, I; Cantini, F; Ciofi-Baffoni, S; Huffman, DL; O'Halloran, TV
    Characterization of the binding interface between the copper chaperone Atx1 and the first cytosolic domain of Ccc2 ATPase
    JOURNAL OF BIOLOGICAL CHEMISTRY
    
    F. Arnesano et al., "Characterization of the binding interface between the copper chaperone Atx1 and the first cytosolic domain of Ccc2 ATPase", J BIOL CHEM, 276(44), 2001, pp. 41365-41376
22. Vanderwerf, SM; Cooper, MJ; Stetsenko, IV; Lutsenko, S
    Copper specifically regulates intracellular phosphorylation of the Wilson's disease protein, a human copper-transporting ATPase
    JOURNAL OF BIOLOGICAL CHEMISTRY
    
    S.M. Vanderwerf et al., "Copper specifically regulates intracellular phosphorylation of the Wilson's disease protein, a human copper-transporting ATPase", J BIOL CHEM, 276(39), 2001, pp. 36289-36294
23. Tsivkovskii, R; MacArthurs, BC; Lutsenko, S
    The Lys(1010)-Lys(1325) fragment of the Wilson's disease protein binds nucleotides and interacts with the N-terminal domain of this protein in a copper-dependent manner
    JOURNAL OF BIOLOGICAL CHEMISTRY
    
    R. Tsivkovskii et al., "The Lys(1010)-Lys(1325) fragment of the Wilson's disease protein binds nucleotides and interacts with the N-terminal domain of this protein in a copper-dependent manner", J BIOL CHEM, 276(3), 2001, pp. 2234-2242
24. Banci, L; Bertini, I; Ciofi-Baffoni, S; Huffman, DL; O'Halloran, TV
    Solution structure of the yeast copper transporter domain Ccc2a in the apoand Cu(I)-loaded states
    JOURNAL OF BIOLOGICAL CHEMISTRY
    
    L. Banci et al., "Solution structure of the yeast copper transporter domain Ccc2a in the apoand Cu(I)-loaded states", J BIOL CHEM, 276(11), 2001, pp. 8415-8426
25. Bal, N; Mintz, E; Guillain, F; Catty, P
    A possible regulatory role for the metal-binding domain of CadA, the Listeria monocytogenes Cd2+-ATPase
    FEBS LETTERS
    
    N. Bal et al., "A possible regulatory role for the metal-binding domain of CadA, the Listeria monocytogenes Cd2+-ATPase", FEBS LETTER, 506(3), 2001, pp. 249-252
26. Multhaup, G; Strausak, D; Bissig, KD; Solioz, M
    Interaction of the CopZ copper chaperone with the CopA copper ATPase of Enterococcus hirae assessed by surface plasmon resonance
    BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS
    
    G. Multhaup et al., "Interaction of the CopZ copper chaperone with the CopA copper ATPase of Enterococcus hirae assessed by surface plasmon resonance", BIOC BIOP R, 288(1), 2001, pp. 172-177
27. Fan, B; Grass, G; Rensing, C; Rosen, BP
    Escherichia coli CopA N-terminal Cys(X)(2)Cys motifs are not required for copper resistance or transport
    BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS
    
    B. Fan et al., "Escherichia coli CopA N-terminal Cys(X)(2)Cys motifs are not required for copper resistance or transport", BIOC BIOP R, 286(2), 2001, pp. 414-418
28. Wu, ZY; Wang, N; Lin, MT; Fang, L; Murong, SX; Yu, L
    Mutation analysis and the correlation between genotype and phenotype of Arg778Leu mutation in Chinese patients with Wilson disease
    ARCHIVES OF NEUROLOGY
    
    Z.Y. Wu et al., "Mutation analysis and the correlation between genotype and phenotype of Arg778Leu mutation in Chinese patients with Wilson disease", ARCH NEUROL, 58(6), 2001, pp. 971-976
29. Xu, PY; Liang, XL; Jankovic, J; Le, W
    Identification of a high frequency of mutation at exon 8 of the ATP7B genein a Chinese population with Wilson disease by fluorescent PCR
    ARCHIVES OF NEUROLOGY
    
    P.Y. Xu et al., "Identification of a high frequency of mutation at exon 8 of the ATP7B genein a Chinese population with Wilson disease by fluorescent PCR", ARCH NEUROL, 58(11), 2001, pp. 1879-1882
30. Rosenzweig, AC
    Copper delivery by metallochaperone proteins
    ACCOUNTS OF CHEMICAL RESEARCH
    
    A.C. Rosenzweig, "Copper delivery by metallochaperone proteins", ACC CHEM RE, 34(2), 2001, pp. 119-128
31. Lee, CC; Wu, JY; Tsai, FJ; Kodama, H; Abe, T; Yang, CF; Tsai, CH
    Molecular analysis of Wilson disease in Taiwan: identification of one novel mutation and evidence of haplotype-mutation association
    JOURNAL OF HUMAN GENETICS
    
    C.C. Lee et al., "Molecular analysis of Wilson disease in Taiwan: identification of one novel mutation and evidence of haplotype-mutation association", J HUM GENET, 45(5), 2000, pp. 275-279
32. Ogawa, A; Yamamoto, S; Kanazawa, M; Ogawa, E; Takayanagi, M; Hasegawa, S; Kohno, Y
    Novel mutation of L718X in the ATP7A gene in a Japanese patient with classical Menkes disease, and four novel polymorphisms in the Japanese population
    JOURNAL OF HUMAN GENETICS
    
    A. Ogawa et al., "Novel mutation of L718X in the ATP7A gene in a Japanese patient with classical Menkes disease, and four novel polymorphisms in the Japanese population", J HUM GENET, 45(5), 2000, pp. 315-317
33. Himelblau, E; Amasino, RM
    Delivering copper within plant cells
    CURRENT OPINION IN PLANT BIOLOGY
    
    E. Himelblau e R.M. Amasino, "Delivering copper within plant cells", CUR OPIN PL, 3(3), 2000, pp. 205-210
34. Sfaello, I; Castelnau, P; Blanc, N; Ogier, H; Evrard, P; Arzimanoglou, A
    Infantile spasms and Menkes disease
    EPILEPTIC DISORDERS
    
    I. Sfaello et al., "Infantile spasms and Menkes disease", EPILEPT DIS, 2(4), 2000, pp. 227-230
35. Selvaag, E
    Pili torti and sensorineural hearing loss. A follow-up of Bjornstad's original patients and a review of the literature
    EUROPEAN JOURNAL OF DERMATOLOGY
    
    E. Selvaag, "Pili torti and sensorineural hearing loss. A follow-up of Bjornstad's original patients and a review of the literature", EUR J DERM, 10(2), 2000, pp. 91-97
36. Loudianos, G; Lovicu, M; Solinas, P; Kanavakis, E; Tzetis, M; Manolaki, N; Panagiotakaki, E; Karpathios, T; Cao, A
    Delineation of the spectrum of Wilson disease mutations in the Greek population and the identification of six novel mutations
    GENETIC TESTING
    
    G. Loudianos et al., "Delineation of the spectrum of Wilson disease mutations in the Greek population and the identification of six novel mutations", GENET TEST, 4(4), 2000, pp. 399-402
37. Wernimont, AK; Huffman, DL; Lamb, AL; O'Halloran, TV; Rosenzweig, AC
    Structural basis for copper transfer by the metallochaperone for the Menkes/Wilson disease proteins
    NATURE STRUCTURAL BIOLOGY
    
    A.K. Wernimont et al., "Structural basis for copper transfer by the metallochaperone for the Menkes/Wilson disease proteins", NAT ST BIOL, 7(9), 2000, pp. 766-771
38. Woeste, KE; Kieber, JJ
    A strong loss-of-function mutation in RAN1 results in constitutive activation of the ethylene response pathway as well as a rosette-lethal phenotype
    PLANT CELL
    
    K.E. Woeste e J.J. Kieber, "A strong loss-of-function mutation in RAN1 results in constitutive activation of the ethylene response pathway as well as a rosette-lethal phenotype", PL CELL, 12(3), 2000, pp. 443-455
39. Olsson, C; Waldenstrom, E; Westermark, K; Landegren, U; Syvanen, AC
    Determination of the frequencies of ten allelic variants of the Wilson disease gene (ATP7B), in pooled DNA samples
    EUROPEAN JOURNAL OF HUMAN GENETICS
    
    C. Olsson et al., "Determination of the frequencies of ten allelic variants of the Wilson disease gene (ATP7B), in pooled DNA samples", EUR J HUM G, 8(12), 2000, pp. 933-938
40. Luo, WQ; Chen, JH; Zhou, HJ; Huang, XW; Zhou, Y; Yuan, JG; Qiang, BQ
    Cloning and expression of a novel human HCUTA cDNA
    CHINESE SCIENCE BULLETIN
    
    W.Q. Luo et al., "Cloning and expression of a novel human HCUTA cDNA", CHIN SCI B, 45(14), 2000, pp. 1301-1304
41. Rinaldi, AC
    Meeting report - Copper research at the top
    BIOMETALS
    
    A.C. Rinaldi, "Meeting report - Copper research at the top", BIOMETALS, 13(1), 2000, pp. 9-13
42. Forbes, JR; Cox, DW
    Copper-dependent trafficking of Wilson disease mutant ATP7B proteins
    HUMAN MOLECULAR GENETICS
    
    J.R. Forbes e D.W. Cox, "Copper-dependent trafficking of Wilson disease mutant ATP7B proteins", HUM MOL GEN, 9(13), 2000, pp. 1927-1935
43. Moller, LB; Petersen, C; Lund, C; Horn, N
    Characterization of the hCTR1 gene: Genomic organization, functional expression, and identification of a highly homologous processed gene
    GENE
    
    L.B. Moller et al., "Characterization of the hCTR1 gene: Genomic organization, functional expression, and identification of a highly homologous processed gene", GENE, 257(1), 2000, pp. 13-22
44. Lee, J; Prohaska, JR; Dagenais, SL; Glover, TW; Thiele, DJ
    Isolation of a murine copper transporter gene, tissue specific expression and functional complementation of a yeast copper transport mutant
    GENE
    
    J. Lee et al., "Isolation of a murine copper transporter gene, tissue specific expression and functional complementation of a yeast copper transport mutant", GENE, 254(1-2), 2000, pp. 87-96
45. Berg, D; Weishaupt, A; Francis, MJ; Miura, N; Yang, XL; Goodyer, ID; Naumann, M; Koltzenburg, M; Reiners, K; Becker, G
    Changes of copper-transporting proteins and ceruloplasmin in the lentiformnuclei in primary adult-onset dystonia
    ANNALS OF NEUROLOGY
    
    D. Berg et al., "Changes of copper-transporting proteins and ceruloplasmin in the lentiformnuclei in primary adult-onset dystonia", ANN NEUROL, 47(6), 2000, pp. 827-830
46. Arredondo, M; Uauy, R; Gonzalez, M
    Regulation of copper uptake and transport in intestinal cell monolayers byacute and chronic copper exposure
    BIOCHIMICA ET BIOPHYSICA ACTA-GENERAL SUBJECTS
    
    M. Arredondo et al., "Regulation of copper uptake and transport in intestinal cell monolayers byacute and chronic copper exposure", BBA-GEN SUB, 1474(2), 2000, pp. 169-176
47. Loudianos, G; Gitlin, JD
    Wilson's disease
    SEMINARS IN LIVER DISEASE
    
    G. Loudianos e J.D. Gitlin, "Wilson's disease", SEM LIV DIS, 20(3), 2000, pp. 353-364
48. Michalczyk, AA; Rieger, J; Allen, KJ; Mercer, JFB; Ackland, ML
    Defective localization of the Wilson disease protein (ATP7B) in the mammary gland of the toxic milk mouse and the effects of copper supplementation
    BIOCHEMICAL JOURNAL
    
    A.A. Michalczyk et al., "Defective localization of the Wilson disease protein (ATP7B) in the mammary gland of the toxic milk mouse and the effects of copper supplementation", BIOCHEM J, 352, 2000, pp. 565-571
49. Reddy, MCM; Majumdar, S; Harris, ED
    Evidence for a Menkes-like protein with a nuclear targeting sequence
    BIOCHEMICAL JOURNAL
    
    M.C.M. Reddy et al., "Evidence for a Menkes-like protein with a nuclear targeting sequence", BIOCHEM J, 350, 2000, pp. 855-863
50. Harris, ED
    Cellular copper transport and metabolism
    ANNUAL REVIEW OF NUTRITION
    
    E.D. Harris, "Cellular copper transport and metabolism", ANN R NUTR, 20, 2000, pp. 291-310
51. Sarkar, B
    Copper transport and its defect in Wilson disease: characterization of thecopper-binding domain of Wilson disease ATPase
    JOURNAL OF INORGANIC BIOCHEMISTRY
    
    B. Sarkar, "Copper transport and its defect in Wilson disease: characterization of thecopper-binding domain of Wilson disease ATPase", J INORG BIO, 79(1-4), 2000, pp. 187-191
52. Kurasaki, M; Okabe, M; Saito, S; Yamanoshita, O; Hosokawa, T; Saito, T
    Histochemical characterization of silver-induced metallothionein in rat kidney
    JOURNAL OF INORGANIC BIOCHEMISTRY
    
    M. Kurasaki et al., "Histochemical characterization of silver-induced metallothionein in rat kidney", J INORG BIO, 78(4), 2000, pp. 275-281
53. Qian, Y; Harris, ED; Zheng, Y; Tiffany-Castiglioni, E
    Lead targets GRP78, a molecular chaperone, in C6 rat glioma cells
    TOXICOLOGY AND APPLIED PHARMACOLOGY
    
    Y. Qian et al., "Lead targets GRP78, a molecular chaperone, in C6 rat glioma cells", TOX APPL PH, 163(3), 2000, pp. 260-266
54. Hirayama, T; Alonso, JM
    Ethylene captures a metal! Metal ions are involved in ethylene perception and signal transduction
    PLANT AND CELL PHYSIOLOGY
    
    T. Hirayama e J.M. Alonso, "Ethylene captures a metal! Metal ions are involved in ethylene perception and signal transduction", PLANT CEL P, 41(5), 2000, pp. 548-555
55. Suzuki, KT; Ogura, Y
    Biological regulation of copper and selective removal of copper: Therapy for Wilson disease and its molecular mechanism
    YAKUGAKU ZASSHI-JOURNAL OF THE PHARMACEUTICAL SOCIETY OF JAPAN
    
    K.T. Suzuki e Y. Ogura, "Biological regulation of copper and selective removal of copper: Therapy for Wilson disease and its molecular mechanism", YAKUGAKU ZA, 120(10), 2000, pp. 899-908
56. Weissman, Z; Berdicevsky, I; Cavari, BZ; Kornitzer, D
    The high copper tolerance of Candida albicans is mediated by a P-type ATPase
    PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA
    
    Z. Weissman et al., "The high copper tolerance of Candida albicans is mediated by a P-type ATPase", P NAS US, 97(7), 2000, pp. 3520-3525
57. Azzouz, M; Poindron, P; Guettier, S; Leclerc, N; Andres, C; Warter, JM; Borg, J
    Prevention of mutant SOD1 motoneuron degeneration by copper chelators in vitro
    JOURNAL OF NEUROBIOLOGY
    
    M. Azzouz et al., "Prevention of mutant SOD1 motoneuron degeneration by copper chelators in vitro", J NEUROBIOL, 42(1), 2000, pp. 49-55
58. Koch, HG; Winterstein, C; Saribas, AS; Alben, JO; Daldal, F
    Roles of the ccoGHIS gene products in the biogenesis of the cbb(3)-type cytochrome c oxidase
    JOURNAL OF MOLECULAR BIOLOGY
    
    H.G. Koch et al., "Roles of the ccoGHIS gene products in the biogenesis of the cbb(3)-type cytochrome c oxidase", J MOL BIOL, 297(1), 2000, pp. 49-65
59. Sharma, R; Rensing, C; Rosen, BP; Mitra, B
    The ATP hydrolytic activity of purified ZntA, a Pb(II)/Cd(II)/Zn(II)-translocating ATPase from Escherichia coli
    JOURNAL OF BIOLOGICAL CHEMISTRY
    
    R. Sharma et al., "The ATP hydrolytic activity of purified ZntA, a Pb(II)/Cd(II)/Zn(II)-translocating ATPase from Escherichia coli", J BIOL CHEM, 275(6), 2000, pp. 3873-3878
60. O'Halloran, TV; Culotta, VC
    Metallochaperones, an intracellular shuttle service for metal ions
    JOURNAL OF BIOLOGICAL CHEMISTRY
    
    T.V. O'Halloran e V.C. Culotta, "Metallochaperones, an intracellular shuttle service for metal ions", J BIOL CHEM, 275(33), 2000, pp. 25057-25060
61. Huffman, DL; O'Halloran, TV
    Energetics of copper trafficking between the Atx1 metallochaperone and theintracellular copper transporter, Ccc2
    JOURNAL OF BIOLOGICAL CHEMISTRY
    
    D.L. Huffman e T.V. O'Halloran, "Energetics of copper trafficking between the Atx1 metallochaperone and theintracellular copper transporter, Ccc2", J BIOL CHEM, 275(25), 2000, pp. 18611-18614
62. Roelofsen, H; Wolters, H; Van Luyn, MJA; Miura, N; Kuipers, F; Vonk, RJ
    Copper-induced apical trafficking of ATP7B in polarized hepatoma cells provides a mechanism for biliary copper excretion
    GASTROENTEROLOGY
    
    H. Roelofsen et al., "Copper-induced apical trafficking of ATP7B in polarized hepatoma cells provides a mechanism for biliary copper excretion", GASTROENTY, 119(3), 2000, pp. 782-793
63. Komatsu, M; Sumizawa, T; Mutoh, M; Chen, ZS; Terada, K; Furukawa, T; Yang, XL; Gao, H; Miura, N; Sugiyama, T; Akiyama, S
    Copper-transporting P-type adenosine triphosphatase (ATP7B) is associated with cisplatin resistance
    CANCER RESEARCH
    
    M. Komatsu et al., "Copper-transporting P-type adenosine triphosphatase (ATP7B) is associated with cisplatin resistance", CANCER RES, 60(5), 2000, pp. 1312-1316
64. DiDonato, M; Hsu, HF; Narindrasorasak, S; Que, L; Sarkar, B
    Copper-induced conformational changes in the N-terminal domain of the Wilson disease copper-transporting ATPase
    BIOCHEMISTRY
    
    M. DiDonato et al., "Copper-induced conformational changes in the N-terminal domain of the Wilson disease copper-transporting ATPase", BIOCHEM, 39(7), 2000, pp. 1890-1896
65. Harada, M; Sakisaka, S; Kawaguchi, T; Kimura, R; Taniguchi, E; Koga, H; Hanada, S; Baba, S; Furuta, K; Kumashiro, R; Sugiyama, T; Sata, M
    Copper does not alter the intracellular distribution of ATP7B, a copper-transporting ATPase
    BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS
    
    M. Harada et al., "Copper does not alter the intracellular distribution of ATP7B, a copper-transporting ATPase", BIOC BIOP R, 275(3), 2000, pp. 871-876
66. Hiromura, M; Chino, H; Sonoda, T; Sakurai, H
    Molecular cloning and characterization of a copper chaperone for copper/zinc superoxide dismutase from the rat
    BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS
    
    M. Hiromura et al., "Molecular cloning and characterization of a copper chaperone for copper/zinc superoxide dismutase from the rat", BIOC BIOP R, 275(2), 2000, pp. 394-400
67. Oyler, RM
    Fragile hair and seizures in a child
    ARCHIVES OF DERMATOLOGY
    
    R.M. Oyler, "Fragile hair and seizures in a child", ARCH DERMAT, 136(3), 2000, pp. 417
68. Tchaparian, EH; Uriu-Adams, JY; Keen, CL; Mitchell, AE; Rucker, RB
    Lysyl oxidase and P-ATPase-7A expression during embryonic development in the rat
    ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS
    
    E.H. Tchaparian et al., "Lysyl oxidase and P-ATPase-7A expression during embryonic development in the rat", ARCH BIOCH, 379(1), 2000, pp. 71-77
69. Urban, Z; Boyd, CD
    Elastic-fiber pathologies: Primary defects in assembly - and secondary disorders in transport and delivery
    AMERICAN JOURNAL OF HUMAN GENETICS
    
    Z. Urban e C.D. Boyd, "Elastic-fiber pathologies: Primary defects in assembly - and secondary disorders in transport and delivery", AM J HU GEN, 67(1), 2000, pp. 4-7
70. Ogawa, A; Yamamoto, S; Takayanagi, M; Kogo, T; Kanazawa, M; Kohno, Y
    An Ile/Val polymorphism at codon 1464 of the ATP7A gene
    JOURNAL OF HUMAN GENETICS
    
    A. Ogawa et al., "An Ile/Val polymorphism at codon 1464 of the ATP7A gene", J HUM GENET, 44(6), 1999, pp. 423-424
71. Ogawa, A; Yamamoto, S; Takayanagi, M; Kogo, T; Kanazawa, M; Kohno, Y
    Identification of three novel mutations in the MNK gene in three unrelatedJapanese patients with classical Menkes disease
    JOURNAL OF HUMAN GENETICS
    
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72. Kodama, H; Murata, Y; Kobayashi, M
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73. Kodama, K; Murata, Y
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74. Suzuki, M; Gitlin, JD
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75. Ho, IC; Lee, TC
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76. Loudianos, G; Dessi, V; Lovicu, M; Angius, A; Figus, A; Lilliu, F; De Virgiliis, S; Nurchi, AM; Deplano, A; Moi, P; Pirastu, M; Cao, AO
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77. Waggoner, DJ; Bartnikas, TB; Gitlin, JD
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78. Rosenzweig, AC; Huffman, DL; Hou, MY; Wernimont, AK; Pufahl, RA; O'Halloran, TV
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79. Buiakova, OI; Xu, J; Lutsenko, S; Zeitlin, S; Das, K; Das, S; Ross, BM; Mekios, C; Scheinberg, IH; Gilliam, TC
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80. De Paepe, A; Loeys, B; Devriendt, K; Fryns, JP
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81. Coutard, M
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82. Harrison, MD; Jones, CE; Dameron, CT
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83. Horn, N; Tumer, Z
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84. Loudianos, G; Dessi, V; Lovicu, M; Angius, A; Pirastu, M; Cao, A
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85. Harris, ED; Reddy, MCM; Majumdar, S
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86. Lu, ZH; Cobine, P; Dameron, CT; Solioz, M
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87. Nanji, MS; Cox, DW
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88. Saito, T; Okabe, M; Hosokawa, T; Kurasaki, M; Hata, A; Endo, F; Nagano, K; Matsuda, I; Urakami, K; Saito, K
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89. Borjigin, J; Payne, AS; Deng, J; Li, XD; Wang, MM; Ovodenko, B; Gitlin, JD; Snyder, SH
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90. Schaefer, M; Gitlin, JD
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91. Jensen, PY; Bonander, N; Moller, LB; Farver, O
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92. Heydorn, K; Damsgaard, E; Horn, N
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93. Multhaup, G; Masters, CL
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94. Abusaad, I; Mohammed, SN; Ogilvie, CM; Ritchie, J; Pohl, KRE; Docherty, Z
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95. Wang, MS; Schinzel, A; Kotzot, D; Balmer, D; Casey, R; Chodirker, BN; Gyftodimou, J; Petersen, MB; Lopez-Rangel, E; Robinson, WP
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96. Ronce, N; Raynaud, M; Toutain, A; Moizard, MP; Colleaux, L; Gendrot, C; Briault, S; Moraine, C
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97. Hirayama, T; Kieber, JJ; Hirayama, N; Kogan, M; Guzman, P; Nourizadeh, S; Alonso, JM; Dailey, WP; Dancis, A; Ecker, JR
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98. Templeton, DM
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99. Qian, YC; Mikeska, G; Harris, ED; Bratton, GR; Tiffany-Castiglioni, E
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100. Seidel, J; Vogt, S; Kirchner, M; Mentzel, HJ; Kauf, E; Zintl, F
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