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Oral administration of glomerular basement membrane prevents the development of experimental autoimmune glomerulonephritis in the WKY rat
JOURNAL OF THE AMERICAN SOCIETY OF NEPHROLOGY
Structure of the human type IV collagen gene COL4A3 and mutations in autosomal Alport syndrome
JOURNAL OF THE AMERICAN SOCIETY OF NEPHROLOGY
Expression and characterization of recombinant rat alpha 3(IV)NC1 and its use in induction of experimental autoimmune glomerulonephritis
NEPHROLOGY DIALYSIS TRANSPLANTATION
T-cell-specific therapy in autoimmune glomerulonephritis - Authors reply
AMERICAN JOURNAL OF KIDNEY DISEASES
The NCI domain of collagen IV encodes a novel network composed of the alpha 1, alpha 2, alpha 5, and alpha 6 chains in smooth muscle basement membranes
JOURNAL OF BIOLOGICAL CHEMISTRY
Helper T cells in antibody-mediated, organ-specific autoimmunity
CURRENT OPINION IN IMMUNOLOGY
Alport syndrome: Abnormalities of type IV collagen genes and proteins
RENAL FAILURE
Ultrastructural appearance of renal and other basement membranes in the bull terrier model of autosomal dominant hereditary nephritis
AMERICAN JOURNAL OF KIDNEY DISEASES
CD28-B7 blockade prevents the development of experimental autoimmune glomerulonephritis
JOURNAL OF CLINICAL INVESTIGATION
Type IV collagen of the glomerular basement membrane - Evidence that the chain specificity of network assembly is encoded by the noncollagenous NC1 domains
JOURNAL OF BIOLOGICAL CHEMISTRY
Abolition of anti-glomerular basement membrane antibody-mediated glomerulonephritis in FcR gamma-deficient mice
EUROPEAN JOURNAL OF IMMUNOLOGY
Rapidly progressive glomerulonephritis
JOURNAL OF NEPHROLOGY
Ultrastructure and composition of Call-Exner bodies in bovine follicles
CELL AND TISSUE RESEARCH
Chain composition of type IV collagen networks in basement membranes
PROCEEDINGS OF THE INDIAN ACADEMY OF SCIENCES-CHEMICAL SCIENCES
Role for transforming growth factor-beta 1 in Alport renal disease progression
KIDNEY INTERNATIONAL
Alport syndrome - An inherited disorder of renal, ocular, and cochlear basement membranes
MEDICINE
Differential tissular expression and localization of type IV collagen alpha(IV), alpha 2(IV), alpha 5(IV), and alpha 6(IV) chains and their mRNA in normal breast and in benign and malignant breast tumors
LABORATORY INVESTIGATION
COMPARATIVE-ANALYSIS OF THE NONCOLLAGENOUS NC1 DOMAIN OF TYPE-IV COLLAGEN - IDENTIFICATION OF STRUCTURAL FEATURES IMPORTANT FOR ASSEMBLY, FUNCTION, AND PATHOGENESIS
Protein science
EXPERIMENTAL AUTOIMMUNE GLOMERULONEPHRITIS (EAG) INDUCED BY HOMOLOGOUS AND HETEROLOGOUS GLOMERULAR-BASEMENT-MEMBRANE IN 2 SUBSTRAINS OF WISTAR-KYOTO RAT
Nephrology, dialysis, transplantation
Anti-glomerular basement membrane nephritis after extracorporeal shock wave lithotripsy
AMERICAN JOURNAL OF NEPHROLOGY
INDUCTION OF ANTI-GBM NEPHRITIS IN RATS BY RECOMBINANT ALPHA-3(IV)NC1AND ALPHA-4(IV)NC1 OF TYPE-IV COLLAGEN
Kidney international
ANTITHYROID AND ANTIADRENAL AUTOANTIBODIES IN ANTIGLOMERULAR BASEMENT-MEMBRANE DISEASE, THIN BASEMENT-MEMBRANE DISEASE AND ALPORT-SYNDROME
Pathology
GLOMERULAR-BASEMENT-MEMBRANE - IDENTIFICATION OF A NOVEL DISULFIDE-CROSS-LINKED NETWORK OF ALPHA-3, ALPHA-4, AND ALPHA-5 CHAINS OF TYPE-IV COLLAGEN AND ITS IMPLICATIONS FOR THE PATHOGENESIS OF ALPORT SYNDROME
The Journal of biological chemistry
THE ULTRASTRUCTURE OF THE LENS CAPSULE ABNORMALITIES IN ALPORTS-SYNDROME
Japanese Journal of Ophthalmology
RECOMBINANT ALPHA-CHAINS OF TYPE-IV COLLAGEN DEMONSTRATE THAT THE AMINO-TERMINAL OF THE GOODPASTURE AUTOANTIGEN IS CRUCIAL FOR ANTIBODY RECOGNITION
Clinical and experimental immunology
Distribution of the alpha 1 to alpha 6 chains of type IV collagen in bovine follicles
BIOLOGY OF REPRODUCTION
ALPORT-SYNDROME - A REVIEW OF THE OCULAR MANIFESTATIONS
Ophthalmic genetics
ALPORTS-SYNDROME - HEREDITARY MUTATIONS I N THE TYPE-IV COLLAGEN FAMILY
MS. Medecine sciences
PURIFICATION AND CHARACTERIZATION OF HUMAN NEPHRITOGENIC ANTIGEN THATINDUCES ANTI-GBM NEPHRITIS IN RATS
Journal of pathology
ISOFORM SWITCHING OF TYPE-IV COLLAGEN IS DEVELOPMENTALLY ARRESTED IN X-LINKED ALPORT SYNDROME LEADING TO INCREASED SUSCEPTIBILITY OF RENAL BASEMENT-MEMBRANES TO ENDOPROTEOLYSIS
The Journal of clinical investigation
A CELL-BINDING DOMAIN FROM THE ALPHA-3 CHAIN OF TYPE-IV COLLAGEN INHIBITS PROLIFERATION OF MELANOMA-CELLS
The Journal of biological chemistry
SEMINIFEROUS TUBULE BASEMENT-MEMBRANE - COMPOSITION AND ORGANIZATION OF TYPE-IV COLLAGEN CHAINS, AND THE LINKAGE OF ALPHA-3(IV) AND ALPHA-5(IV) CHAINS
The Journal of biological chemistry
DIFFERENTIAL EXPRESSION OF ALPHA-1(IV), ALPHA-2(IV), ALPHA-5(IV) AND ALPHA-6(IV) COLLAGEN CHAINS IN THE BASEMENT-MEMBRANE OF BASAL-CELL CARCINOMA
Histochemical Journal
ACUTE-RENAL-FAILURE IN A 21-YEAR-OLD WOMAN
The American journal of medicine
A NOVEL METHOD FOR PRODUCTION OF MONOCLONAL-ANTIBODIES - EVALUATION AND EXPECTATION OF THE RAT LYMPH-NODE METHOD IN CELL AND MOLECULAR-BIOLOGY
Cell biology international
NEPHRITOGENICITY AND ALPHA-CHAIN COMPOSITION OF NC1 FRACTIONS OF TYPE-IV COLLAGEN FROM BOVINE RENAL BASEMENT-MEMBRANE
Virchows Archiv
IDENTIFICATION OF POSTTRANSPLANT ANTI-ALPHA-5(IV) COLLAGEN ALLOANTIBODIES IN X-LINKED ALPORT SYNDROME
Nephrology, dialysis, transplantation
COLLAGEN COL4A3 KNOCKOUT - A MOUSE MODEL FOR AUTOSOMAL ALPORT SYNDROME
Genes & development
EPITOPE MAPPING OF HOMOLOGOUS AND CROSS-REACTIVE ANTIGENS BY MONOCLONAL-ANTIBODIES TO STREPTOCOCCAL CELL-MEMBRANE (MAB TO SCM)
Molecular immunology
EXPERIMENTAL ANTI-GBM GLOMERULONEPHRITIS INDUCED IN RATS BY IMMUNIZATION WITH SYNTHETIC PEPTIDES BASED ON 6 ALPHA-CHAINS OF HUMAN TYPE-IV COLLAGEN
Journal of pathology
DIRECT IDENTIFICATION OF NATURALLY PROCESSED AUTOANTIGEN-DERIVED PEPTIDES BOUND TO HLA-DR15
The Journal of biological chemistry
COORDINATE GENE-EXPRESSION OF THE ALPHA-3, ALPHA-4, AND ALPHA-5 CHAINS OF COLLAGEN TYPE-IV - EVIDENCE FROM A CANINE MODEL OF X-LINKED NEPHRITIS WITH A COL4A5 GENE MUTATION
The Journal of biological chemistry
THE ROLE OF T-LYMPHOCYTES IN EXTRACAPILLARY GLOMERULONEPHRITIS
JN. Journal of nephrology
AUTOSOMAL RECESSIVE ALPORT SYNDROME - MUTATION IN THE COL4A3 GENE IN A WOMAN WITH ALPORT SYNDROME AND POSTTRANSPLANT ANTIGLOMERULAR BASEMENT-MEMBRANE NEPHRITIS
Journal of the American Society of Nephrology
SPLICE-MEDIATED INSERTION OF AN ALU SEQUENCE IN THE COL4A3 MESSENGER-RNA CAUSING AUTOSOMAL RECESSIVE ALPORT SYNDROME
Human molecular genetics
ESTABLISHMENT BY THE RAT LYMPH-NODE METHOD OF EPITOPE-DEFINED MONOCLONAL-ANTIBODIES RECOGNIZING THE 6 DIFFERENT ALPHA-CHAINS OF HUMAN TYPE-IV COLLAGEN
HISTOCHEMISTRY AND CELL BIOLOGY
GLOMERULONEPHRITIS WITH ANTIGLOMERULAR BASEMENT-MEMBRANE ANTIBODY DURING PREGNANCY - POTENTIAL ROLE OF THE PLACENTA IN AMELIORATION OF DISEASE
American journal of kidney diseases
A COL4A3 GENE MUTATION AND POSTTRANSPLANT ANTI-ALPHA-3(IV) COLLAGEN ALLOANTIBODIES IN ALPORT SYNDROME
Kidney international
BULL TERRIER HEREDITARY NEPHRITIS - A MODEL FOR AUTOSOMAL-DOMINANT ALPORT SYNDROME
Kidney international
DIFFERENTIAL DISTRIBUTION OF TYPE-IV COLLAGEN CHAINS IN PATIENTS WITHDIABETIC NEPHROPATHY IN NON-INSULIN-DEPENDENT DIABETES-MELLITUS
Nephron
IMMUNOHISTOLOGICAL LOCALIZATION OF THE NOVEL EPITOPE RELATED TO TYPE-IV COLLAGEN IN NORMAL AND DISEASED RENAL TISSUES
Journal of pathology
DIFFERENTIAL EXPRESSION OF 2 BASEMENT-MEMBRANE COLLAGEN GENES, COL4A6AND COL4A5, DEMONSTRATED BY IMMUNOFLUORESCENCE STAINING USING PEPTIDE-SPECIFIC MONOCLONAL-ANTIBODIES
The Journal of cell biology
AUTOANTIBODIES IN NEPHROLOGY
Der Internist
CHARACTERIZATION AND EXPRESSION OF MULTIPLE ALTERNATIVELY SPLICED TRANSCRIPTS OF THE GOODPASTURE ANTIGEN GENE REGION - GOODPASTURE ANTIBODIES RECOGNIZE RECOMBINANT PROTEINS REPRESENTING THE AUTOANTIGEN AND ONEOF ITS ALTERNATIVE FORMS
European journal of biochemistry
IDENTIFICATION OF MUTATIONS IN THE ALPHA-3(IV) AND ALPHA-4(IV) COLLAGEN GENES IN AUTOSOMAL RECESSIVE ALPORT SYNDROME
Nature genetics
IDENTIFICATION OF THE GOODPASTURE ANTIGEN, ALPHA-3(IV) NC1, AND 4 OTHER NC1 DOMAINS OF TYPE-IV COLLAGEN, BY AMINO-TERMINAL SEQUENCE-ANALYSIS OF HUMAN GLOMERULAR-BASEMENT-MEMBRANE SEPARATED BY 2-DIMENSIONAL ELECTROPHORESIS
Experimental nephrology
INHERITED DISEASES OF THE GLOMERULAR-BASEMENT-MEMBRANE
American journal of kidney diseases
IMMUNOHISTOCHEMICAL STUDY OF ALPHA-1-5 CHAINS OF TYPE-IV COLLAGEN IN HEREDITARY NEPHRITIS
Kidney international
COL4A5 GENE DELETION AND PRODUCTION OF POSTTRANSPLANT ANTI-ALPHA-3(IV) COLLAGEN ALLOANTIBODIES IN ALPORT SYNDROME
Kidney international
THE IMMUNOGENETICS OF GLOMERULONEPHRITIS
Kidney international
CANINE X-CHROMOSOME-LINKED HEREDITARY NEPHRITIS - A GENETIC MODEL FORHUMAN X-LINKED HEREDITARY NEPHRITIS RESULTING FROM A SINGLE-BASE MUTATION IN THE GENE ENCODING THE ALPHA-5 CHAIN OF COLLAGEN TYPE-IV
Proceedings of the National Academy of Sciences of the United Statesof America
COLLAGEN-IV ALPHA-3-CHAIN, ALPHA-4-CHAIN, AND ALPHA-5-CHAIN IN RODENTBASAL LAMINAE - SEQUENCE, DISTRIBUTION, ASSOCIATION WITH LAMININS, AND DEVELOPMENTAL SWITCHES
The Journal of cell biology
COLLAGEN-IV ALPHA-3-CHAIN, ALPHA-4-CHAIN, AND ALPHA-5-CHAIN IN RODENTBASAL LAMINAE - SEQUENCE, DISTRIBUTION, ASSOCIATION WITH LAMININS, AND DEVELOPMENTAL SWITCHES
The Journal of cell biology
COMPLETE PRIMARY STRUCTURE OF THE HUMAN TYPE-IV COLLAGEN ALPHA-4(IV) CHAIN - COMPARISON WITH STRUCTURE AND EXPRESSION OF THE OTHER ALPHA(IV) CHAINS
The Journal of biological chemistry
THE ALPHA-3 CHAIN OF TYPE-IV COLLAGEN PREVENTS ACTIVATION OF HUMAN POLYMORPHONUCLEAR LEUKOCYTES
The Journal of biological chemistry
COMPLETE PRIMARY STRUCTURE OF THE HUMAN ALPHA-3(IV) COLLAGEN CHAIN - COEXPRESSION OF THE ALPHA-3(IV) AND ALPHA-4(IV) COLLAGEN CHAINS IN HUMAN TISSUES
The Journal of biological chemistry
ALTERNATIVE SPLICING OF THE NC1 DOMAIN OF THE HUMAN-ALPHA-3(IV) COLLAGEN GENE - DIFFERENTIAL EXPRESSION OF MESSENGER-RNA TRANSCRIPTS THAT PREDICT 3 PROTEIN VARIANTS WITH DISTINCT CARBOXYL REGIONS
The Journal of biological chemistry
IDENTIFICATION OF A CELL LINEAGE-SPECIFIC GENE CODING FOR A SEA-URCHIN ALPHA-2(IV)-LIKE COLLAGEN CHAIN
The Journal of biological chemistry
COMPLETE PRIMARY STRUCTURE OF THE 6TH CHAIN OF HUMAN BASEMENT-MEMBRANE COLLAGEN, ALPHA-6(IV) - ISOLATION OF THE CDNAS FOR ALPHA-6(IV) AND COMPARISON WITH 5 OTHER TYPE-IV COLLAGEN CHAINS
The Journal of biological chemistry
IDENTIFICATION OF A NEW COLLAGEN-IV CHAIN, ALPHA-6(IV), BY CDNA ISOLATION AND ASSIGNMENT OF THE GENE TO CHROMOSOME XQ22, WHICH IS THE SAME LOCUS FOR COL4A5
The Journal of biological chemistry
IN-VIVO TREATMENT WITH A MONOCLONAL-ANTIBODY TO T-HELPER CELLS IN EXPERIMENTAL AUTOIMMUNE GLOMERULONEPHRITIS IN THE BN RAT
Clinical and experimental immunology
TYPE-IV COLLAGEN ALPHA-5 CHAIN - NORMAL-DISTRIBUTION AND ABNORMALITIES IN X-LINKED ALPORT SYNDROME REVEALED BY MONOCLONAL-ANTIBODY
The American journal of pathology
THE ROLE OF T-HELPER LYMPHOCYTES IN PRIMING FOR EXPERIMENTAL AUTOIMMUNE GLOMERULONEPHRITIS IN THE BN RAT
Journal of autoimmunity
ALPORT SYNDROME - FROM BEDSIDE TO GENOME TO BEDSIDE
American journal of kidney diseases
PROLIFERATIVE AUTOIMMUNE GLOMERULONEPHRITIS IN RATS - A MODEL FOR AUTOIMMUNE GLOMERULONEPHRITIS IN HUMANS
Kidney international
THE GOODPASTURE ANTIGEN - COMMON EPITOPES IN THE GLOBULAR DOMAINS OF COLLAGEN-IV
Nephron
CDNA ISOLATION AND PARTIAL GENE STRUCTURE OF THE HUMAN ALPHA-4(IV) COLLAGEN CHAIN
FEBS letters
STRUCTURE AND COMPOSITION OF TYPE-IV COLLAGEN OF BOVINE AORTA
Biochimica et biophysica acta