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Processing of beta-dystroglycan by matrix metalloproteinase disrupts the link between the extracellular matrix and cell membrane via the dystroglycancomplex
HUMAN MOLECULAR GENETICS
Muscular dystrophy in female dogs
JOURNAL OF VETERINARY INTERNAL MEDICINE
The dystroglycan complex is necessary for stabilization of acetylcholine receptor clusters at neuromuscular junctions and formation of the synaptic basement membrane
JOURNAL OF CELL BIOLOGY
Dysbindin, a novel coiled-coil-containing protein that interacts with the dystrobrevins in muscle and brain
JOURNAL OF BIOLOGICAL CHEMISTRY
Biochemical evidence for association of dystrobrevin with the sarcoglycan-sarcospan complex as a basis for understanding sarcoglycanopathy
HUMAN MOLECULAR GENETICS
Aquaporin-4 is absent at the sarcolemma and at perivascular astrocyte endfeet in alpha 1-syntrophin knockout mice
PROCEEDINGS OF THE JAPAN ACADEMY SERIES B-PHYSICAL AND BIOLOGICAL SCIENCES
Differential expression of dystrophin, utrophin, and dystrophin-associatedproteins in human muscle culture
CELL AND TISSUE RESEARCH
Current knowledge of dystrophin and dystrophin-associated proteins in the retina
HISTOLOGY AND HISTOPATHOLOGY
Dystrobrevin localization in photoreceptor axon terminals and at blood-ocular barrier sites
INVESTIGATIVE OPHTHALMOLOGY & VISUAL SCIENCE
Neural regulation of alpha-dystroglycan biosynthesis and glycosylation in skeletal muscle
JOURNAL OF NEUROCHEMISTRY
Disruption of heart sarcoglycan complex and severe cardiomyopathy caused by beta sarcoglycan mutations
JOURNAL OF MEDICAL GENETICS
alpha-dystroglycan isoforms are differentially distributed in adult rat retina
JOURNAL OF COMPARATIVE NEUROLOGY
Adhesion-dependent tyrosine phosphorylation of beta-dystroglycan regulatesits interaction with utrophin
JOURNAL OF CELL SCIENCE
Loss of dystrophin and some dystrophin-associated proteins with concomitant signs of apoptosis in rat leg muscle overworked in extension
ACTA NEUROPATHOLOGICA
Interaction of a PDZ protein domain with a synthetic library of all human protein C termini
ANGEWANDTE CHEMIE-INTERNATIONAL EDITION
Functional roles of dystrophin and of associated proteins. New insights for the sarcoglycans
ITALIAN JOURNAL OF NEUROLOGICAL SCIENCES
O-mannosyl glycans in mammals
BIOCHIMICA ET BIOPHYSICA ACTA-GENERAL SUBJECTS
Localization of sodium and potassium currents at sites of nerve-muscle contact in embryonic Xenopus muscle cells in culture
PFLUGERS ARCHIV-EUROPEAN JOURNAL OF PHYSIOLOGY
Could utrophin rescue the myocardium of patients with dystrophin gene mutations?
JOURNAL OF MOLECULAR AND CELLULAR CARDIOLOGY
alpha-dystroglycan is a laminin receptor involved in extracellular matrix assembly on myotubes and muscle cell viability
JOURNAL OF CELL BIOLOGY
Ecto-ATPase activity of alpha-sarcoglycan (adhalin)
JOURNAL OF BIOLOGICAL CHEMISTRY
Trends in skeletal muscle biology and the understanding of toughness in beef
AUSTRALIAN JOURNAL OF AGRICULTURAL RESEARCH
EX-VIVO GENE-TRANSFER USING ADENOVIRUS-MEDIATED FULL-LENGTH DYSTROPHIN DELIVERY TO DYSTROPHIC MUSCLES
Gene therapy
UTROPHIN IS A REGENERATION-ASSOCIATED PROTEIN TRANSIENTLY PRESENT AT THE SARCOLEMMA OF REGENERATING SKELETAL-MUSCLE FIBERS IN DYSTROPHIN-DEFICIENT HYPERTROPHIC FELINE MUSCULAR-DYSTROPHY
Journal of neuropathology and experimental neurology
Molecular organization of sarcoglycan complex in mouse myotubes in culture
JOURNAL OF CELL BIOLOGY
ROLE OF ACTIN-BINDING PROTEIN IN INSERTION OF ADHESION RECEPTORS INTOTHE MEMBRANE
The Journal of biological chemistry
INCREASED CAVEOLIN-3 LEVELS IN MDX MOUSE MUSCLES
FEBS letters
RECENT ADVANCES IN DIAGNOSIS OF THE CHILDHOOD MUSCULAR-DYSTROPHIES
Journal of paediatrics and child health
DP140 - ALTERNATIVELY SPLICED ISOFORMS IN BRAIN AND KIDNEY
Genomics
ASSOCIATION OF MUSCLE-SPECIFIC KINASE MUSK WITH THE ACETYLCHOLINE-RECEPTOR IN MAMMALIAN MUSCLE
EMBO journal
DISTRIBUTION OF INTRAMEMBRANOUS PARTICLE-SIZE IN THE MUSCLE PLASMA-MEMBRANE OF THE MDX MOUSE
Journal of the neurological sciences
LAMININ-INDUCED CLUSTERING OF DYSTROGLYCAN ON EMBRYONIC MUSCLE-CELLS - COMPARISON WITH AGRIN-INDUCED CLUSTERING
The Journal of cell biology
A ROLE OF DYSTROGLYCAN IN SCHWANNOMA CELL-ADHESION TO LAMININ
The Journal of biological chemistry
THE 4TH COMPONENT OF THE SARCOGLYCAN COMPLEX
FEBS letters
CONCOMITANT DEFICIENCY OF BETA-SARCOGLYCANS AND GAMMA-SARCOGLYCANS IN20 ALPHA-SARCOGLYCAN (ADHALIN)-DEFICIENT PATIENTS - IMMUNOHISTOCHEMICAL ANALYSIS AND CLINICAL ASPECTS
Acta Neuropathologica
DYSTROGLYCAN - AN EXTRACELLULAR-MATRIX RECEPTOR-LINKED TO THE CYTOSKELETON
Current opinion in cell biology
RECEPTORS FOR LAMININS DURING EPITHELIAL MORPHOGENESIS
Current opinion in cell biology
DYSTROPHIN-GLYCOPROTEIN COMPLEX PURIFIED FROM HAMSTER CARDIAC-MUSCLE - COMPARISON OF THE COMPLEXES FROM CARDIAC AND SKELETAL-MUSCLES OF HAMSTER AND RABBIT
Journal of Molecular and Cellular Cardiology
DYSTROPHIN-ASSOCIATED PROTEIN ABNORMALITIES IN DYSTROPHIN-DEFICIENT MUSCLE-FIBERS FROM SYMPTOMATIC AND ASYMPTOMATIC DUCHENNE BECKER MUSCULAR-DYSTROPHY CARRIERS/
Acta Neuropathologica
A SYNTROPHIN GENE MAPS TO MOUSE CHROMOSOME-8 AND IS NOT THE MYODYSTROPHY GENE
Mammalian genome
TEMPORAL AND SPATIAL APPEARANCE OF ALPHA-DYSTROGLYCAN IN DIFFERENTIATED MOUSE MYOBLASTS IN CULTURE
Journal of cellular biochemistry
LIMB-GIRDLE MUSCULAR-DYSTROPHY - CLINICAL AND PATHOLOGICAL REEVALUATION
Journal of the neurological sciences
A MUTATION IN THE DYSTROPHIN GENE SELECTIVELY AFFECTING DYSTROPHIN EXPRESSION IN THE HEART
The Journal of clinical investigation
EXPRESSION OF DYSTROPHIN-ASSOCIATED GLYCOPROTEINS AND UTROPHIN IN CARRIERS OF DUCHENNE MUSCULAR-DYSTROPHY
Neuromuscular disorders
EXPRESSION OF DYSTROPHIN-ASSOCIATED GLYCOPROTEINS DURING HUMAN FETAL MUSCLE DEVELOPMENT - A PRELIMINARY IMMUNOCYTOCHEMICAL STUDY
Neuromuscular disorders
EXPRESSION OF DYSTROPHIN-ASSOCIATED PROTEINS TN DYSTROPHIN-POSITIVE MUSCLE-FIBERS (REVERTANTS) IN DUCHENNE MUSCULAR-DYSTROPHY
Neuromuscular disorders
DEFICIENCY OF THE 50 KDA DYSTROPHIN-ASSOCIATED GLYCOPROTEIN AND ABNORMAL EXPRESSION OF UTROPHIN IN 2 SOUTH ASIAN COUSINS WITH VARIABLE EXPRESSION OF SEVERE CHILDHOOD AUTOSOMAL RECESSIVE MUSCULAR-DYSTROPHY
Neuromuscular disorders
GENETIC-HETEROGENEITY OF SEVERE CHILDHOOD AUTOSOMAL RECESSIVE MUSCULAR-DYSTROPHY WITH ADHALIN (50 KDA DYSTROPHY-ASSOCIATED GLYCOPROTEIN) DEFICIENCY
Comptes rendus de l'Academie des sciences. Serie 3, Sciences de la vie
BUILDING SYNAPSES - AGRIN AND DYSTROGLYCAN STICK TOGETHER
Trends in neurosciences
DYSTROPHIN-GLYCOPROTEIN COMPLEX - ITS ROLE IN THE MOLECULAR PATHOGENESIS OF MUSCULAR-DYSTROPHIES
Muscle & nerve
HUMAN ADHALIN IS ALTERNATIVELY SPLICED AND THE GENE IS LOCATED ON CHROMOSOME 17Q21
Proceedings of the National Academy of Sciences of the United Statesof America
AUTOSOMAL RECESSIVE DISTAL MUSCULAR-DYSTROPHY - NORMAL EXPRESSION OF DYSTROPHIN, UTROPHIN AND DYSTROPHIN-ASSOCIATED PROTEINS IN MUSCLE-FIBERS
Journal of the neurological sciences
IMMUNOHISTOCHEMICAL ANALYSIS OF DYSTROPHIN-ASSOCIATED PROTEINS IN BECKER DUCHENNE MUSCULAR-DYSTROPHY WITH HUGE IN-FRAME DELETIONS IN THE NH2-TERMINAL AND ROD DOMAINS OF DYSTROPHIN/
The Journal of clinical investigation
IMMUNOGOLD LOCALIZATION OF THE 43-KDA DYSTROGLYCAN AT THE PLASMA-MEMBRANE IN CONTROL AND DYSTROPHIC HUMAN MUSCLE
Acta Neuropathologica
DEFICIENCY OF DYSTROPHIN-ASSOCIATED PROTEINS IN DUCHENNE MUSCULAR-DYSTROPHY PATIENTS LACKING COOH-TERMINAL DOMAINS OF DYSTROPHIN
The Journal of clinical investigation