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PPAR-alpha and PPAR-gamma activators induce cholesterol removal from humanmacrophage foam cells through stimulation of the ABCA1 pathway
NATURE MEDICINE
MR virtual angioscopy of thoracic aortic atherosclerosis in homozygous familial hypercholesterolemia
JOURNAL OF COMPUTER ASSISTED TOMOGRAPHY
Executive summary of the Third Report of the National Cholesterol Education Program (NCEP) expert panel on detection, evaluation, and treatment of high blood cholesterol in adults (Adult Treatment Panel III)
JAMA-JOURNAL OF THE AMERICAN MEDICAL ASSOCIATION
Regulation and intracellular trafficking of the ABCA1 transporter
JOURNAL OF LIPID RESEARCH
ABCA1 overexpression leads to hyperalphalipoproteinemia and increased biliary cholesterol excretion in transgenic mice
JOURNAL OF CLINICAL INVESTIGATION
Cellular localization and trafficking of the human ABCA1 transporter
JOURNAL OF BIOLOGICAL CHEMISTRY
Analysis of glomerulosclerosis and atherosclerosis in lecithin cholesterolacyltransferase-deficient mice
JOURNAL OF BIOLOGICAL CHEMISTRY
Apolipoprotein specificity for lipid efflux by the human ABCAI transporter
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS
Erdheim-Chester disease: A rare multisystem histiocytic disorder associated with interstitial lung disease
AMERICAN JOURNAL OF THE MEDICAL SCIENCES
Two genes that map to the STSL locus cause sitosterolemia: genomic structure and spectrum of mutations involving sterolin-1 and sterolin-2, encoded by ABCG5 and ABCG8, respectively
AMERICAN JOURNAL OF HUMAN GENETICS
In vivo evidence for both lipolytic and nonlipolytic function of hepatic lipase in the metabolism of HDL
ARTERIOSCLEROSIS THROMBOSIS AND VASCULAR BIOLOGY
LCAT modulates atherogenic plasma lipoproteins and the extent of atherosclerosis only in the presence of normal LDL receptors in transgenic rabbits
ARTERIOSCLEROSIS THROMBOSIS AND VASCULAR BIOLOGY
Lecithin-cholesterol acyltransferase: role in lipoprotein metabolism, reverse cholesterol transport and atherosclerosis
CURRENT OPINION IN LIPIDOLOGY
Complete genomic sequence of the human ABCA1 gene: Analysis of the human and mouse ATP-binding cassette A promoter
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA
Hepatic lipase deficiency decreases the selective uptake of HDL-cholesteryl esters in vivo
JOURNAL OF LIPID RESEARCH
The lipid-laden foam cell: an elusive target for therapeutic intervention
JOURNAL OF CLINICAL INVESTIGATION
Tangier disease is caused by mutations in the gene encoding ATP-binding cassette transporter 1
NATURE GENETICS
Human ATP-binding cassette transporter 1 (ABC1): Genomic organization and identification of the genetic defect in the original Tangier disease kindred
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA
Cubilin, the endocytic receptor for intrinsic factor-vitamin B-12 complex,mediates high-density lipoprotein holoparticle endocytosis
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA
Hepatic lipase promotes the selective uptake of high density lipoprotein-cholesteryl esters via the scavenger receptor B1
JOURNAL OF LIPID RESEARCH
Cholesteryl ester transfer protein corrects dysfunctional high density lipoproteins and reduces aortic atherosclerosis in lecithin cholesterol acyltransferase transgenic mice
JOURNAL OF BIOLOGICAL CHEMISTRY
Hypertriglyceridemia: Changes in the plasma lipoproteins associated with an increased risk of cardiovascular disease
AMERICAN JOURNAL OF CARDIOLOGY
Genetic disorders of high-density lipoprotein metabolism
LIPOPROTEINS IN HEALTH AND DISEASE
HOEG,JEFFREY,M., MD - IN-MEMORIAM
Endocrinology and metabolism clinics of North America
UP-REGULATED SYNTHESIS OF BOTH APOLIPOPROTEIN-A-I AND APOLIPOPROTEIN-B IN FAMILIAL HYPERALPHALIPOPROTEINEMIA AND HYPERBETALIPOPROTEINEMIA
Metabolism, clinical and experimental
CORRECTION OF HYPOALPHALIPOPROTEINEMIA IN LDL RECEPTOR-DEFICIENT RABBITS BY LECITHIN-CHOLESTEROL ACYLTRANSFERASE
Journal of lipid research
DIFFERENTIAL RATE OF CHOLESTEROL EFFLUX FROM THE APICAL AND BASOLATERAL MEMBRANES OF MDCK CELLS
Journal of lipid research
Hepatic lipase facilitates the selective uptake of cholesteryl esters fromremnant lipoproteins in apoE-deficient mice
JOURNAL OF LIPID RESEARCH
CHARACTERIZATION OF HIGH-DENSITY LIPOPROTEIN-BOUND AND SOLUBLE RT6 RELEASED FOLLOWING ADMINISTRATION OF ANTI-RT6.1 MONOCLONAL-ANTIBODY
The Journal of immunology (1950)
DELAYED LOW-DENSITY-LIPOPROTEIN (LDL) CATABOLISM DESPITE A FUNCTIONALINTACT LDL-APOLIPOPROTEIN-B PARTICLE AND LDL-RECEPTOR IN A SUBJECT WITH CLINICAL HOMOZYGOUS FAMILIAL HYPERCHOLESTEROLEMIA
The Journal of clinical endocrinology and metabolism
ADENOVIRUS-MEDIATED EXPRESSION OF LCAT IN NONHUMAN-PRIMATES LEADS TO AN ANTIATHEROGENIC LIPOPROTEIN PROFILE WITH INCREASED HDL AND DECREASED LDL
Circulation
CLA-1 SR-B1 - IN-VIVO EVIDENCE FOR SELECTIVE UPTAKE OF CHOLESTEROL ESTERS FROM APO-B REMNANT LIPOPROTEINS IN APOE DEFICIENT MICE/
Circulation
APOA-I AND APOA-II METABOLISM IN HYPERALPHALIPOPROTEINEMIA INDUCED BYETOH
Circulation
EXPRESSION OF HUMAN APOA-L ABOLISHES AORTIC ATHEROSCLEROSIS IN LCAT-TRANSGENIC MICE
Circulation
EFFECTS OF DYSFUNCTIONAL HDL ON CHOLESTEROL EFFLUX IN LCAT TRANSGENICMICE
Circulation
SQUALENE SYNTHASE PROMOTER COUPLED TO A SECRETORY REPORTER - A NOVEL SYSTEM FOR MONITORING THE REGULATORY POOL OF CHOLESTEROL IN CELLS
Circulation
VITAMIN-E DOSE-RESPONSE STUDIES IN HUMANS WITH USE OF DEUTERATED RRR-ALPHA-TOCOPHEROL
The American journal of clinical nutrition
DECREASED REVERSE CHOLESTEROL TRANSPORT FROM TANGIER DISEASE FIBROBLASTS - ACCEPTOR SPECIFICITY AND EFFECT OF BREFELDIN ON LIPID EFFLUX
Arteriosclerosis, thrombosis, and vascular biology
THERAPEUTIC RESPONSE TO MEDIUM-CHAIN TRIGLYCERIDES AND OMEGA-3-FATTY-ACIDS IN A PATIENT WITH THE FAMILIAL CHYLOMICRONEMIA SYNDROME
Arteriosclerosis, thrombosis, and vascular biology
LIPOPROTEIN-LIPASE CORRELATES POSITIVELY AND HEPATIC LIPASE INVERSELYWITH CALCIFIC ATHEROSCLEROSIS IN HOMOZYGOUS FAMILIAL HYPERCHOLESTEROLEMIA
Arteriosclerosis, thrombosis, and vascular biology
HIGH PLASMA HDL CONCENTRATIONS ASSOCIATED WITH ENHANCED ATHEROSCLEROSIS IN TRANSGENIC MICE OVEREXPRESSING LECITHIN-CHOLESTERYL ACYLTRANSFERASE
Nature medicine
INJECTION OF ANTI-RT6.1 ANTIBODIES INTO DIABETES-RESISTANT RATS INCREASES PLASMA RT6 ALLOANTIGEN
The FASEB journal
ADENOVIRUS-MEDIATED EXPRESSION OF HEPATIC LIPASE IN LCAT TRANSGENIC MICE
Journal of lipid research
INTRACELLULAR TRAFFICKING OF THE FREE-CHOLESTEROL DERIVED FROM LDL CHOLESTERYL ESTER IS DEFECTIVE IN-VIVO IN NIEMANN-PICK-C-DISEASE - INSIGHTS ON NORMAL METABOLISM OF HDL AND LDL GAINED FROM THE NP-C MUTATION
Journal of lipid research
OVEREXPRESSION OF HUMAN LECITHIN-CHOLESTEROL ACYLTRANSFERASE IN CHOLESTEROL-FED RABBITS - LDL METABOLISM AND HDL METABOLISM ARE AFFECTED INA GENE DOSE-DEPENDENT MANNER
Journal of lipid research
PLASMA PHOSPHOLIPID TRANSFER PROTEIN - ADENOVIRUS-MEDIATED OVEREXPRESSION IN MICE LEADS TO DECREASED PLASMA HIGH-DENSITY-LIPOPROTEIN (HDL) AND ENHANCED HEPATIC-UPTAKE OF PHOSPHOLIPIDS AND CHOLESTERYL ESTERS FROM HDL
The Journal of biological chemistry
TARGETED DISRUPTION OF THE MOUSE LECITHIN-CHOLESTEROL ACYLTRANSFERASE(LCAT) GENE - GENERATION OF A NEW ANIMAL-MODEL FOR HUMAN LCAT DEFICIENCY
The Journal of biological chemistry
GENE TARGETS FOR TREATMENT OF CARDIOVASCULAR-DISEASE
Atherosclerosis
CORRECTION OF HYPOALPHALIPOPROTEINEMIA IN LDL RECEPTOR DEFICIENCY BY LECITHIN-CHOLESTEROL ACYLTRANSFERASE (LCAT)
Atherosclerosis
THE IN-VIVO OF METABOLISM OF FREE-APO(A) IN NORMALS AND SUBJECTS WITHABETALIPOPROTEINEMIA
Atherosclerosis
HUMAN LECITHIN-CHOLESTEROL ACYLTRANSFERASE DEFICIENCY - IN-VIVO LPX KINETICS AND ITS CELL ASSOCIATION WITH VARIOUS CELLS
Atherosclerosis
LECITHIN-CHOLESTEROL ACYLTRANSFERASE (LCAT) KNOCKOUT MICE - A NEW ANIMAL-MODEL FOR HUMAN LCAT-DEFICIENCY
Atherosclerosis
2 NOVEL MUTATIONS OF CHOLESTERYL ESTER TRANSFER PROTEIN (CETP) GENE IN JAPANESE HYPERALPHALIPOPROTEINEMIC PATIENTS
Atherosclerosis
RELATIVE IMPORTANCE OF APOE IN CHOLESTEROL EFFLUX
Atherosclerosis
DIFFERENTIAL CHOLESTEROL EFFLUX FROM PLASMA-MEMBRANE DOMAINS OF EPITHELIAL-CELLS
Clinical chemistry
IDENTIFICATION OF A RESIDUE (433K) ESSENTIAL FOR HEPATIC LIPASE-MEDIATED REMNANT LIPOPROTEIN METABOLISM INDEPENDENT OF LIPOLYSIS
Circulation
THE EFFECT OF HEPATIC LIPASE DEFICIENCY ON THE PLASMA-LIPIDS, LIPOPROTEINS AND DIET-INDUCED ATHEROSCLEROSIS IN LCAT TRANSGENIC MICE
Circulation
CETP MODULATES THE DEVELOPMENT OF AORTIC ATHEROSCLEROSIS IN LCAT-TRANSGENIC MICE
Circulation
ANALYSIS OF AORTIC ATHEROSCLEROSIS AND GLOMERULOSCLEROSIS IN LCAT KNOCKOUT MICE
Circulation
OVEREXPRESSION OF LCAT IN TRANSGENIC RABBITS ENHANCES LDL CATABOLISM VIA THE LDL RECEPTOR PATHWAY
Circulation
THE IN-VIVO METABOLISM OF APOLIPOPROTEIN E-CONTAINING HIGH-DENSITY-LIPOPROTEINS
Circulation
LECITHIN-CHOLESTEROL ACYLTRANSFERASE DEFICIENCY - HUMAN IN-VIVO KINETICS OF LDL, APOA-I AND APOA-II IN PARTIAL LCAT DEFICIENCY (FISH EYE DISEASE) WITH AND WITHOUT CAD
Circulation
GENE-THERAPY FOR ATHEROSCLEROSIS SECONDARY TO GENETIC DYSLIPOPROTEINEMIAS BY OVEREXPRESSION OF HEPATIC LIPASE AND APOLIPOPROTEIN-A-I
American journal of human genetics
HOMOZYGOUS FAMILIAL HYPOBETALIPOPROTEINEMIA - INCREASED LDL CATABOLISM IN HYPOBETALIPOPROTEINEMIA DUE TO A TRUNCATED APOLIPOPROTEIN-B SPECIES, APO B-87(PADOVA)
Arteriosclerosis, thrombosis, and vascular biology
ALZHEIMER A-BETA NEUROTOXICITY - PROMOTION BY ANTICHYMOTRYPSIN, APOE4- INHIBITION BY A-BETA-RELATED PEPTIDES
Neurobiology of aging
OVEREXPRESSION OF LECITHIN, CHOLESTEROL ACYLTRANSFERASE IN TRANSGENICRABBITS PREVENTS DIET-INDUCED ATHEROSCLEROSIS
Proceedings of the National Academy of Sciences of the United Statesof America
ADENOVIRAL DELIVERY OF LOW-DENSITY-LIPOPROTEIN RECEPTORS TO HYPERLIPIDEMIC RABBITS - RECEPTOR EXPRESSION MODULATES HIGH-DENSITY-LIPOPROTEINS
Metabolism, clinical and experimental
APOA-II KINETICS IN HUMANS USING ENDOGENOUS LABELING WITH STABLE ISOTOPES - SLOWER TURNOVER OF APOA-II COMPARED WITH THE EXOGENOUS RADIOTRACER METHOD
Journal of lipid research
HYPERALPHALIPOPROTEINEMIA IN HUMAN LECITHIN-CHOLESTEROL ACYLTRANSFERASE TRANSGENIC RABBITS - IN-VIVO APOLIPOPROTEIN-A-I CATABOLISM IS DELAYED IN A GENE DOSE-DEPENDENT MANNER
The Journal of clinical investigation
HEPATIC LIPASE GENE-THERAPY IN HEPATIC LIPASE-DEFICIENT MICE - ADENOVIRUS-MEDIATED REPLACEMENT OF A LIPOLYTIC ENZYME TO THE VASCULAR ENDOTHELIUM
The Journal of clinical investigation
LECITHIN-CHOLESTEROL ACYLTRANSFERASE OVEREXPRESSION GENERATES HYPERALPHA-LIPOPROTEINEMIA AND A NONATHEROGENIC LIPOPROTEIN PATTERN IN TRANSGENIC RABBITS
The Journal of biological chemistry
DEFECTIVE REVERSE CHOLESTEROL TRANSPORT IN TANGIER DISEASE SKIN FIBROBLASTS
Clinical chemistry
LP(A) - COMPARISON OF THE IN-VIVO METABOLISM OF APO(A) AND LP(A) IN MAN
Circulation
LECITHIN-HOLESTEROL ACYLTRANSFERASE (LCAT) KNOCKOUT MICE - A NEW ANIMAL-MODEL FOR HUMAN LCAT-DEFICIENCY
Circulation
LCAT OVEREXPRESSION MODULATES THE METABOLISM OF APOLIPOPROTEIN B-CONTAINING LIPOPROTEINS IN TRANSGENIC RABBITS
Circulation
LECITHIN-CHOLESTEROL ACYLTRANSFERASE DEFICIENCY - HUMAN IN-VIVO KINETICS OF LDL AND LPX-LIKE LIPOPROTEINS
Circulation
PHOSPHOLIPID TRANSFER PROTEIN - ADENOVIRUS-MEDIATED OVEREXPRESSION INMICE LEADS TO DECREASED PLASMA HDL, INCREASED VLDL-LDL AND ACCELERATED HEPATIC-UPTAKE OF HDL PHOSPHOLIPIDS
Circulation
ADENOVIRUS-MEDIATED TRANSFER OF HEPATIC LIPASE (HL) IN TRANSGENIC RABBITS OVEREXPRESSING HUMAN LECITHIN-CHOLESTEROL ACYLTRANSFERASE (LCAT)
Circulation
IN-VIVO EVIDENCE FOR A NONLIPOLYTIC HOLE OF HEPATIC LIPASE IN THE METABOLISM OF HIGH-DENSITY-LIPOPROTEINS
Circulation
ADENOVIRUS-MEDIATED EXPRESSION OF HEPATIC LIPASE IN APOE DEFICIENT MICE - EVIDENCE FOR HEPATIC LIPASE-MEDIATED CLEARANCE OF REMNANT LIPOPROTEIN
Circulation
APOLIPOPROTEIN-E - THE DIFFERENTIAL EFFECT OF APOE AND LPE PARTICLES IN CHOLESTEROL EFFLUX
Circulation
OVEREXPRESSION OF HUMAN LECITHIN-CHOLESTEROL ACYLTRANSFERASE (LCAT) IN LCAT TRANSGENIC AND APO-E DEFICIENT MICE LEADS TO ENHANCED ATHEROSCLEROSIS
Circulation
APOLIPOPROTEIN A-II PRODUCTION-RATE IS A MAJOR FACTOR REGULATING THE DISTRIBUTION OF APOLIPOPROTEIN-A-I AMONG HDL SUBCLASSES LPA-I AND LPA-I-A-II IN NORMOLIPIDEMIC HUMANS
Arteriosclerosis, thrombosis, and vascular biology
A PILOT-STUDY OF EX-VIVO GENE-THERAPY FOR HOMOZYGOUS FAMILIAL HYPERCHOLESTEROLEMIA
Nature medicine
DEFECTIVE APOLIPOPROTEIN-MEDIATED CHOLESTEROL AND PHOSPHOLIPID EFFLUXFROM TANGIER DISEASE FIBROBLASTS
Molecular biology of the cell
IDENTIFICATION OF NOVEL DIFFERENTIALLY EXPRESSED HEPATIC GENES IN CHOLESTEROL-FED RABBITS BY A NON-TARGETED GENE APPROACH
Journal of lipid research
INCREASED CATABOLIC RATE OF LOW-DENSITY LIPOPROTEINS IN HUMANS WITH CHOLESTERYL ESTER TRANSFER PROTEIN-DEFICIENCY
The Journal of clinical investigation
APOLIPOPROTEIN-E DEFICIENCY IN MICE - GENE REPLACEMENT AND PREVENTIONOF ATHEROSCLEROSIS USING ADENOVIRUS VECTORS
The Journal of clinical investigation
DOMINANT EXPRESSION OF TYPE-III HYPERLIPOPROTEINEMIA - PATHOPHYSIOLOGICAL INSIGHTS DERIVED FROM THE STRUCTURAL AND KINETIC CHARACTERISTICS OF APOE-1(LYS(146)-]GLU)
The Journal of clinical investigation
THE LOW-DENSITY-LIPOPROTEIN RECEPTOR IS NOT REQUIRED FOR NORMAL CATABOLISM OF LP(A) IN HUMANS
The Journal of clinical investigation
OVEREXPRESSION OF HUMAN LECITHIN-CHOLESTEROL ACYLTRANSFERASE LEADS TOHYPERALPHALIPOPROTEINEMIA IN TRANSGENIC MICE
The Journal of biological chemistry
IN-VITRO EXPRESSION OF STRUCTURAL DEFECTS IN THE LECITHIN-CHOLESTEROLACYLTRANSFERASE GENE
The Journal of biological chemistry
CARBOXYL-TERMINAL DOMAIN TRUNCATION ALTERS APOLIPOPROTEIN-A-I IN-VIVOCATABOLISM
The Journal of biological chemistry
LIPOPROTEINS CONTAINING APOLIPOPROTEIN-B ISOLATED FROM PATIENTS WITH ABETALIPOPROTEINEMIA AND HOMOZYGOUS HYPOBETALIPOPROTEINEMIA - IDENTIFICATION AND CHARACTERIZATION
Atherosclerosis
LIPOPROTEIN (A) IN PATIENTS WITH HYPERLIPIDEMIA
European journal of clinical investigation
CHARACTERIZATION OF HIGH-DENSITY APOLIPOPROTEIN PARTICLES A-I AND A-I-A-II ISOLATED FROM HUMANS WITH CHOLESTERYL ESTER TRANSFER PROTEIN-DEFICIENCY
European journal of biochemistry
ISOLATION OF NOVEL DIETARY-CHOLESTEROL REGULATED GENES FROM A PCR-BASED SUBTRACTION LIBRARY OF RABBIT LIVER
Clinical chemistry
APOE AND APOA-II METABOLISM IN TRANSGENIC MICE OVEREXPRESSING APOA-II
Circulation
LCAT MODULATES DIETARY-LIPID RESPONSE IN HLCAT TRANSGENIC RABBITS
Circulation
LECITHIN-CHOLESTEROL ACYL TRANSFERASE TRANSGENIC RABBITS - HYPERALPHALIPOPROTEINEMIA AND DIET-INDUCED ATHEROSCLEROSIS
Circulation