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Paroxysmal nocturnal hemoglobinuria: Insights from recent advances in molecular biology
TRANSFUSION MEDICINE REVIEWS
The RNA component of telomerase is mutated in autosomal dominant dyskeratosis congenita
NATURE
FES-Cre targets phosphatidylinositol glycan class A (PIGA) inactivation tohematopoietic stem cells in the bone marrow
JOURNAL OF EXPERIMENTAL MEDICINE
Cytogenetic and morphological abnormalities in paroxysmal nocturnal haemoglobinuria
BRITISH JOURNAL OF HAEMATOLOGY
GATA1-Cre mediates Piga gene inactivation in the erythroid/megakaryocytic lineage and leads to circulating red cells with a partial deficiency in glycosyl phosphatidylinositol-linked proteins (paroxysmal nocturnal hemoglobinuria type II cells)
BLOOD
A technique of stapled gastrojejunostomy for open gastric bypass results in increased wound complication-rate
OBESITY SURGERY
Port site tumor recurrence rates in a murine model of laparoscopic splenectomy decreased with increased experience
SURGICAL ENDOSCOPY-ULTRASOUND AND INTERVENTIONAL TECHNIQUES
A serum-soluble factor(s) stimulates tumor growth following laparotomy in a murine model
SURGICAL ENDOSCOPY-ULTRASOUND AND INTERVENTIONAL TECHNIQUES
Lymphocyte proliferation in mice after a full laparotomy is the same whether performed in a sealed carbon dioxide chamber or in room air
SURGICAL ENDOSCOPY-ULTRASOUND AND INTERVENTIONAL TECHNIQUES
Time course of differences in lymphocyte proliferation rates after laparotomy vs CO2 insufflation
SURGICAL ENDOSCOPY-ULTRASOUND AND INTERVENTIONAL TECHNIQUES
Increased tumor establishment and growth after open vs laparoscopic surgery in mice may be related to differences in postoperative T-cell function
SURGICAL ENDOSCOPY-ULTRASOUND AND INTERVENTIONAL TECHNIQUES
Delayed-type hypersensitivity response is better preserved in mice following insufflation than after laparotomy
SURGICAL ENDOSCOPY-ULTRASOUND AND INTERVENTIONAL TECHNIQUES
X inactivation and somatic cell selection rescue female mice carrying a Piga-null mutation
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA
Tumor proliferative index is higher in mice undergoing laparotomy vs. CO2 pneumoperitoneum
DISEASES OF THE COLON & RECTUM
Peritoneal irrigation with povidone-iodine solution after laparoscopic-assisted splenectomy significantly decreases port-tumor recurrence in a murinemodel
DISEASES OF THE COLON & RECTUM
Increased sensitivity to complement and a decreased red blood cell life span in mice mosaic for a nonfunctional Piga gene
BLOOD
THE SPECTRUM OF SOMATIC MUTATIONS IN THE PIG-A GENE IN PAROXYSMAL-NOCTURNAL HEMOGLOBINURIA INCLUDES LARGE DELETIONS AND SMALL DUPLICATIONS
Blood cells, molecules, & diseases (Print)
WOUND TENSILE-STRENGTH AND CONTRACTION RATE ARE NOT AFFECTED BY LAPAROTOMY OR PNEUMOPERITONEUM
Surgical endoscopy
INCREASED TUMOR ESTABLISHMENT AND GROWTH AFTER OPEN VS LAPAROSCOPIC BOWEL RESECTION IN MICE
Surgical endoscopy
METABOLISM AND IMMUNOLOGY IN LAPAROSCOPY - FIRST WORKSHOP ON EXPERIMENTAL LAPAROSCOPIC SURGERY, FRANKFURT, 1997
Surgical endoscopy
TRAUMATIC HANDLING OF THE TUMOR INDEPENDENT OF PNEUMOPERITONEUM INCREASES PORT SITE IMPLANTATION RATE OF COLON-CANCER IN A MURINE MODEL
Surgical endoscopy
THE EFFECT OF PERITONEAL AIR EXPOSURE ON POSTOPERATIVE TUMOR-GROWTH
Surgical endoscopy
THE EFFECTS OF ELEVATED INTRAABDOMINAL PRESSURE, HYPERCARBIA, AND POSITIONING ON THE HEMODYNAMIC-RESPONSES TO LAPAROSCOPIC COLECTOMY IN PIGS
Surgical endoscopy
TUMOR IMPLANTATION AT LAPAROSCOPY - IS IT A REAL PROBLEM
Surgical endoscopy
SOMATIC MUTATION AND CLONAL SELECTION IN THE PATHOGENESIS AND IN THE CONTROL OF PAROXYSMAL-NOCTURNAL HEMOGLOBINURIA
Seminars in hematology
PREOPERATIVE EUS VERSUS INTRAOPERATIVE CHOLANGIOGRAM IN PATIENTS WITHSUSPECTED COMMON BILE-DUCT STONES - A PROSPECTIVE RANDOMIZED TRIAL
Gastrointestinal endoscopy
ABDOMINAL WOUND TUMOR RECURRENCE AFTER OPEN AND LAPAROSCOPIC-ASSISTEDSPLENECTOMY IN A MURINE MODEL
Diseases of the colon & rectum
COLON ADENOCARCINOMA AND B-16 MELANOMA GROW LARGER FOLLOWING LAPAROTOMY VS. PNEUMOPERITONEUM IN A MURINE MODEL
Diseases of the colon & rectum
HEMATOPOIESIS DEFICIENT IN GPI-LINKED PROTEINS IN MICE CHIMERIC FOR ANONFUNCTIONAL PIG-A GENE
British Journal of Haematology
NEW SOMATIC MUTATION IN THE PIG-A GENE EMERGES AT RELAPSE OF PAROXYSMAL-NOCTURNAL HEMOGLOBINURIA
Blood
A PROSPECTIVE COMPARISON OF LAPAROSCOPIC EXPOSURE TECHNIQUES FOR RECTAL MOBILIZATION AND SIGMOID RESECTION
Journal of the American College of Surgeons
A MURINE MODEL OF LAPAROSCOPIC-ASSISTED INTERVENTION
Surgical endoscopy
POSTOPERATIVE IMMUNE FUNCTION VARIES INVERSELY WITH THE DEGREE OF SURGICAL TRAUMA IN A MURINE MODEL
Surgical endoscopy
HELIUM-NEON LASER IRRADIATION AT FLUENCES OF 1, 2, AND 4 J CM(2) FAILED TO ACCELERATE WOUND-HEALING AS ASSESSED BY BOTH WOUND CONTRACTURE RATE AND TENSILE-STRENGTH/
Lasers in surgery and medicine
SOMATIC MUTATIONS IN PAROXYSMAL-NOCTURNAL HEMOGLOBINURIA - A BLESSINGIN DISGUISE
Cell
MURINE EMBRYONIC STEM-CELLS WITHOUT PIG-A GENE ACTIVITY ARE COMPETENTFOR HEMATOPOIESIS WITH THE PNH PHENOTYPE BUT NOT FOR CLONAL EXPANSION
The Journal of clinical investigation
CHROMOSOMAL-ABNORMALITIES IN PAROXYSMAL-NOCTURNAL HEMOGLOBINURIA (PNH)
Blood
SEARCH FOR GENETIC-FACTORS THROMBOSIS IN PAROXYSMAL-NOCTURNAL HEMOGLOBINURIA - THE POSSIBLE ROLE OF A MUTANT METHYLENETETRAHYDROFOLATE REDUCTASE (C677T)
Blood
PNH-LIKE LYMPHOCYTES ARE COMPETENT FOR GENERATING THE ENTIRE IMMUNE-SYSTEM IN RAG NULL MICE
Blood
SURVEY OF MUTATIONS OF THE PIG-A GENE IN PAROXYSMAL-NOCTURNAL HEMOGLOBINURIA - PHENOTYPE-GENOTYPE CORRELATIONS
Blood
INACTIVATION OF PIG-A IN HEMATOPOIETIC STEM-CELLS OBTAINED BY CRE-LOXP MEDIATED RECOMBINATION - A MOUSE MODEL FOR PNH
Blood
MUTATIONS OF THE PIG-A GENE IN PAROXYSMAL-NOCTURNAL HEMOGLOBINURIA (PNH) - AN UPDATE SURVEY
American journal of human genetics
TRANSLUMINAL AORTIC-VALVE PLACEMENT - A FEASIBILITY STUDY WITH A NEWLY DESIGNED COLLAPSIBLE AORTIC-VALVE
ASAIO journal
CONTROLLED TRIAL OF LAPAROSCOPIC-ASSISTED VS OPEN COLON RESECTION IN A PORCINE MODEL
Surgical endoscopy
FACTOR-V LEIDEN MUTATION INVESTIGATED BY AMPLIFICATION CREATED RESTRICTION ENZYME SITE (ACRES) IN PNH PATIENTS WITH AND WITHOUT THROMBOSIS
Haematologica
EMBRYONIC STEM-CELLS DEFECTIVE IN THE PIG-A GENE SHOW HEMATOPOIETIC DIFFERENTIATION IN-VITRO
Experimental hematology
MICE WITH HEMATOPOIESIS DEFICIENT IN GLYCOSYL PHOSPHATIDYLINOSITOL (GPI) LINKED MOLECULES - A POSSIBLE MODEL FOR PAROXYSMAL-NOCTURNAL HEMOGLOBINURIA (PNH)
Experimental hematology
BETTER PRESERVATION OF IMMUNE FUNCTION AFTER LAPAROSCOPIC-ASSISTED VSOPEN BOWEL RESECTION IN A MURINE MODEL
Diseases of the colon & rectum
CELL-CELL INTERACTION AMONG PIG-A NULL EMBRYONIC STEM-CELLS IN-VITRO MAY FAVOR THEIR HEMATOPOIETIC DIFFERENTIATION
Blood
HEMATOPOIESIS WITH THE PNH PHENOTYPE IN MICE CHIMERIC FOR A NON FUNCTIONAL PIG-A GENE
Blood
INCREASED TUMOR ESTABLISHMENT AND GROWTH AFTER LAPAROTOMY VS LAPAROSCOPY - REPLY
Archives of surgery
A NEW METHOD TO PREVENT PORT DISLODGMENT DURING LAPAROSCOPIC SURGERY
Surgical endoscopy
TUMOR-GROWTH AFTER LAPAROTOMY OR LAPAROSCOPY - A PRELIMINARY-STUDY
Surgical endoscopy
LAPAROSCOPIC HARVESTING OF JEJUNAL FREE FLAPS
Annals of plastic surgery
NATURAL-HISTORY OF PAROXYSMAL-NOCTURNAL HEMOGLOBINURIA
The New England journal of medicine
MUTATIONS IN THE PIG-A GENE CAUSING PAROXYSMAL-NOCTURNAL HEMOGLOBINURIA ARE MAINLY OF THE FRAMESHIFT TYPE
Blood
FACTOR-V LEIDEN MUTATION INVESTIGATED BY A MODIFIED PCR TECHNIQUE IN PNH PATIENTS WITH THROMBOSIS
Blood
THE COMPLEX NATURE OF SOMATIC MUTATIONS IN PAROXYSMAL-NOCTURNAL HEMOGLOBINURIA
Blood
INCREASED TUMOR ESTABLISHMENT AND GROWTH AFTER LAPAROTOMY VS LAPAROSCOPY IN A MURINE MODEL
Archives of surgery
MOLECULAR HETEROGENEITY OF SOMATIC MUTATIONS IN PAROXYSMAL-NOCTURNAL HEMOGLOBINURIA (PNA)
American journal of human genetics
GENOMIC ORGANIZATION OF THE X-LINKED GENE (PIG-A) THAT IS MUTATED IN PAROXYSMAL-NOCTURNAL HEMOGLOBINURIA AND OF A RELATED AUTOSOMAL PSEUDOGENE MAPPED TO 12Q21
Human molecular genetics
IS IMMUNE FUNCTION BETTER PRESERVED AFTER LAPAROSCOPIC VERSUS OPEN COLON RESECTION
Surgical endoscopy
PRESERVATION OF IMMUNE-RESPONSE AFTER LAPAROSCOPY
Surgical endoscopy
PAROXYSMAL-NOCTURNAL HEMOGLOBINURIA (PNH) IS CAUSED BY SOMATIC MUTATIONS IN THE PIG-A GENE
EMBO journal
SOMATIC MUTATIONS AND CELLULAR-SELECTION IN PAROXYSMAL-NOCTURNAL HEMOGLOBINURIA
Lancet
MUTATIONS IN THE PIG-A GENE CAUSING PARTIAL DEFICIENCY OF GPI-LINKED SURFACE-PROTEINS (PNH-II) IN PATIENTS WITH PAROXYSMAL-NOCTURNAL HEMOGLOBINURIA
British Journal of Haematology
MYELODYSPLASIA IN A PATIENT WITH PREEXISTING PAROXYSMAL-NOCTURNAL HEMOGLOBINURIA - A CLONAL DISEASE ORIGINATING FROM WITHIN A CLONAL DISEASE
British Journal of Haematology
EXPRESSION OF RECOMBINANT TRANSMEMBRANE CD59 IN PAROXYSMAL-NOCTURNAL HEMOGLOBINURIA B-CELLS CONFERS RESISTANCE TO HUMAN-COMPLEMENT
Blood
MUTATIONS IN THE PIG-A GENE CAUSING PAROXYSMAL-NOCTURNAL HEMOGLOBINURIA (PNH) ARE MAINLY OF THE FRAMESHIFT TYPE
Blood
PAROXYSMAL-NOCTURNAL HEMOGLOBINURIA - CORRECTION OF ABNORMAL PHENOTYPE BY SOMATIC-CELL HYBRIDIZATION
Somatic cell and molecular genetics
MEMBRANE-PROTEINS IN PAROXYSMAL-NOCTURNAL HEMOGLOBINURIA
Blood reviews
INTRAOPERATIVE FLUORESCEIN ANGIOGRAPHY
Ophthalmology
SPECIFIC DEFECT IN N-ACETYLGLUCOSAMINE INCORPORATION IN THE BIOSYNTHESIS OF THE GLYCOSYLPHOSPHATIDYLINOSITOL ANCHOR IN CLONED CELL-LINES FROM PATIENTS WITH PAROXYSMAL-NOCTURNAL HEMOGLOBINURIA
Proceedings of the National Academy of Sciences of the United Statesof America
SEARCH FOR THE MOLECULAR LESION OF PAROXYSMAL-NOCTURNAL HEMOGLOBINURIA
British Journal of Haematology
MYELODYSPLASIA IN A PATIENT WITH PREEXISTING PAROXYSMAL-NOCTURNAL HEMOGLOBINURIA - A CLONAL DISEASE WITHIN A CLONAL DISEASE
British Journal of Haematology
THE IDENTIFICATION OF THE BIOCHEMICAL DEFECT IN CELL-LINES FROM 9 PATIENTS WITH PAROXYSMAL-NOCTURNAL HEMOGLOBINURIA
British Journal of Haematology
LONG-TERM FOLLOW-UP OF 80 PATIENTS WITH PNH - 11 OF 32 PATIENTS SURVIVING 10 YEARS ACHIEVE SPONTANEOUS REMISSION
Blood
HETEROGENEITY OF MOLECULAR LESIONS IN PATIENTS WITH PAROXYSMAL-NOCTURNAL HEMOGLOBINURIA
Blood