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Titolo:
Clinical features of isolated noncompaction of the myocardium in children
Autore:
Neudorf, UE; Hussein, A; Trowitzsch, E; Schmaltz, AA;
Indirizzi:
Univ Essen Gesamthsch, Dept Pediat Cardiol, Essen, Germany Univ Essen Gesamthsch Essen Germany Dept Pediat Cardiol, Essen, Germany Univ Witten Herdecke, Vest Kinderklin, Dept Pediat Cardiol, Witten, Germany Univ Witten Herdecke Witten Germany ept Pediat Cardiol, Witten, Germany
Titolo Testata:
CARDIOLOGY IN THE YOUNG
fascicolo: 4, volume: 11, anno: 2001,
pagine: 439 - 442
SICI:
1047-9511(200107)11:4<439:CFOINO>2.0.ZU;2-D
Fonte:
ISI
Lingua:
ENG
Soggetto:
LEFT-VENTRICULAR MYOCARDIUM; SPONGY MYOCARDIUM; NON-COMPACTION; PERSISTENCE;
Keywords:
spongy myocardium; cardiac transplantation; absence of the spleen;
Tipo documento:
Article
Natura:
Periodico
Settore Disciplinare:
Clinical Medicine
Citazioni:
14
Recensione:
Indirizzi per estratti:
Indirizzo: Neudorf, UE Univ Hosp, Dept Pediat Cardiol, Hufelandstr 55, D-45122 Essen,Germany Univ Hosp Hufelandstr 55 Essen Germany D-45122 Essen, Germany
Citazione:
U.E. Neudorf et al., "Clinical features of isolated noncompaction of the myocardium in children", CARD YOUNG, 11(4), 2001, pp. 439-442

Abstract

Isolated noncompaction of the myocardium, also known as "spongy myocardium", is a rare disease in children and adults. It is suggested that, during early development of the heart, the primary spongy structure persists due toan arrest of compaction. No other cardiac malformations are found, but there are familial occurences, relations to genetic disorders or syndromes such as Melnick-needles-syndrome or Xq28-linked cardiomyopathy, and reports ofconduction disorders. We have now diagnosed isolated noncompaction in seven children aged between five weeks and 5.5 years. Three are doing well with anticongestive therapy, while transplantation of the heart was performed in one. Three of the children have died, but in only one case due to cardiac failure. Our experience emphasises the need rapidly to establish the diagnosis, to search for associated extracardiac abnormalities, and to consider transplantation at an early stage.

ASDD Area Sistemi Dipartimentali e Documentali, Università di Bologna, Catalogo delle riviste ed altri periodici
Documento generato il 18/01/20 alle ore 11:32:51