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Titolo:
Parry-Romberg and Rasmussen's syndromes: are the similarities just coincidental?
Autore:
Straube, A; Padovan, CS; Seelos, K;
Indirizzi:
Univ Munich, Abt Neuroradiol, Munich, Germany Univ Munich Munich Germany niv Munich, Abt Neuroradiol, Munich, Germany
Titolo Testata:
NERVENARZT
fascicolo: 8, volume: 72, anno: 2001,
pagine: 641 - 646
SICI:
0028-2804(200108)72:8<641:PARSAT>2.0.ZU;2-C
Fonte:
ISI
Lingua:
ENG
Soggetto:
PROGRESSIVE FACIAL HEMIATROPHY; GLUTAMATE-RECEPTOR GLUR3; ENCEPHALITIS;
Keywords:
autoimmune disease; central neurological complications; hemiatrophy; Parry-Romberg syndrome; Rasmussen's syndrome; scleroderma; vasculitis;
Tipo documento:
Article
Natura:
Periodico
Settore Disciplinare:
Clinical Medicine
Citazioni:
26
Recensione:
Indirizzi per estratti:
Indirizzo: Straube, A Klinikum Grosshadern, Marchioninistr 15, D-81377 Munich, Germany Klinikum Grosshadern Marchioninistr 15 Munich Germany D-81377
Citazione:
A. Straube et al., "Parry-Romberg and Rasmussen's syndromes: are the similarities just coincidental?", NERVENARZT, 72(8), 2001, pp. 641-646

Abstract

The Parry-Romberg syndrome is a rare and poorly understood disease characterized by slowly progressive, localized atrophy of the skin,subcutaneous tissue, muscles, and bones. The atrophy is typically localized in the face and begins in youth. In some patients, imaging can show the lesions and atrophy of the ipsilateral hemisphere of the brain. We report on a patient in whom the disease has lasted 36 years and discuss the possibility that the Parry-Romberg syndrome is related to known autoimmune disorders of the soft tissue (e.g., linear scleroderma) and Rasmussen's syndrome. There are some remarkable clinical similarities between these two syndromes, including age of onset, unilateral manifestation, and occurrence of focal seizures. It is most probable that both diseases have an autoimmunological background.

ASDD Area Sistemi Dipartimentali e Documentali, Università di Bologna, Catalogo delle riviste ed altri periodici
Documento generato il 25/05/20 alle ore 04:50:33