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Titolo:
Familial association of congenital left heart abnormalities and sustained fetal arrhythmia
Autore:
Hajdu, J; Marton, T; Toth-Pal, E; Papp, Z;
Indirizzi:
Semmelweis Univ Med, Sch Med, Dept Obstet & Gynecol 1, H-1088 Budapest, Hungary Semmelweis Univ Med Budapest Hungary H-1088 1, H-1088 Budapest, Hungary
Titolo Testata:
PEDIATRIC CARDIOLOGY
fascicolo: 5, volume: 20, anno: 1999,
pagine: 368 - 370
SICI:
0172-0643(199909/10)20:5<368:FAOCLH>2.0.ZU;2-Y
Fonte:
ISI
Lingua:
ENG
Soggetto:
FORAMEN OVALE; DIAGNOSIS;
Keywords:
hypoplastic left heart; fetal ectopic atrial tachycardia; fetal echocardiography; familial association;
Tipo documento:
Article
Natura:
Periodico
Settore Disciplinare:
Clinical Medicine
Citazioni:
17
Recensione:
Indirizzi per estratti:
Indirizzo: Hajdu, J Semmelweis Univ Med, Sch Med, Dept Obstet & Gynecol 1, Baross Str27, H-1088 Budapest, Hungary Semmelweis Univ Med Baross Str 27 Budapest Hungary H-1088 ungary
Citazione:
J. Hajdu et al., "Familial association of congenital left heart abnormalities and sustained fetal arrhythmia", PEDIAT CARD, 20(5), 1999, pp. 368-370

Abstract

Hypoplastic left heart syndrome (HLHS) is the most common cause of death from heart disease in the first week of life. There are reports about familial concordance by presumed morphogenetic mechanisms of abnormal embryonic blood flow with phenotypes of varying severity. The risk of having a child with a left heart lesion after a previously affected child may be as high as5% to 12%. We present case reports from four families in which sustained fetal arrhythmia (three ectopic atrial tachycardias and one severe bradycardia due to excessive ectopic atrial beats) was demonstrated. Within these four families a close relative of the mother (a previous child, a brother, ora nephew) had severe left heart abnormality (three with HLHS and one with severe aortic valve stenosis). The association of sustained fetal arrhythmia of ectopic atrial origin and severe left heart abnormalities could be expected to occur by chance in a very low percentage of cases. We conclude that sustained fetal atrial ectopic arrhythmia is a congenital abnormality andshould be considered as a risk factor for inherited congenital heart abnormalities.

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Documento generato il 30/11/20 alle ore 03:36:27