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Titolo:
Prolonged QT interval in Rett syndrome
Autore:
Ellaway, CJ; Sholler, G; Leonard, H; Christodoulou, J;
Indirizzi:
Univ Sydney, Dept Paediat & Child Hlth, Sydney, NSW 2006, Australia Univ Sydney Sydney NSW Australia 2006 d Hlth, Sydney, NSW 2006, Australia Royal24,exandra Hosp Children, Western Sydney Genet Program, Sydney, NSW 21 Royal Alexandra Hosp Children Sydney NSW Australia 2124 m, Sydney, NSW 21 Royal Alexandra Hosp Children, Adolph Basser Cardiac Inst, Camperdown, NSW, Royal Alexandra Hosp Children Camperdown NSW Australia Camperdown, NSW, TVW Telethon, Inst Child Hlth Res, W Perth, WA 6827, Australia TVW Telethon W Perth WA Australia 6827 h Res, W Perth, WA 6827, Australia
Titolo Testata:
ARCHIVES OF DISEASE IN CHILDHOOD
fascicolo: 5, volume: 80, anno: 1999,
pagine: 470 - 472
SICI:
0003-9888(199905)80:5<470:PQIIRS>2.0.ZU;2-E
Fonte:
ISI
Lingua:
ENG
Soggetto:
CRITERIA; DEATH;
Keywords:
Rett syndrome; prolonged QT; electrocardiography;
Tipo documento:
Article
Natura:
Periodico
Settore Disciplinare:
Clinical Medicine
Life Sciences
Citazioni:
13
Recensione:
Indirizzi per estratti:
Indirizzo: Christodoulou, J Univ Sydney, Dept Paediat & Child Hlth, Sydney, NSW 2006,Australia Univ Sydney Sydney NSW Australia 2006 SW 2006, Australia
Citazione:
C.J. Ellaway et al., "Prolonged QT interval in Rett syndrome", ARCH DIS CH, 80(5), 1999, pp. 470-472

Abstract

Rett syndrome is a severe neurodevelopmental disorder of unknown aetiology. A prolonged QT interval has been described previously in patients with Rett syndrome. To investigate QT prolongation and the presence of cardiac tachyarrhythmias in Rett syndrome electrocardiography and 24 hour Holter monitoring were performed prospectively in a cohort of 34 girls with Rett syndrome. The corrected QT value was prolonged in nine patients. Compared with a group of healthy controls of a similar age range, the patients with Rett syndrome had significantly longer corrected QT values. Clinical severity was not a predictor for prolonged QT intervals in the Rett syndrome cohort. Theprolonged QT syndrome is a serious and potentially lethal cardiac disorderand should be considered in all girls with Rett syndrome.

ASDD Area Sistemi Dipartimentali e Documentali, Università di Bologna, Catalogo delle riviste ed altri periodici
Documento generato il 26/01/20 alle ore 22:09:08