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Titolo:
CECAL VOLVULUS IN THE CORNELIA-DE-LANGE-SYNDROME
Autore:
HUSAIN K; FITZGERALD P; LAU G;
Indirizzi:
CHILDRENS HOSP CHEDOKE MCMASTER,DIV PEDIAT SURG,ROOM 4E-2,1200 MAIN ST W HAMILTON L8N 3Z5 ON CANADA CHILDRENS HOSP CHEDOKE MCMASTER,DIV PEDIAT SURG HAMILTON L8N 3Z5 ON CANADA
Titolo Testata:
Journal of pediatric surgery
fascicolo: 9, volume: 29, anno: 1994,
pagine: 1245 - 1247
SICI:
0022-3468(1994)29:9<1245:CVITC>2.0.ZU;2-R
Fonte:
ISI
Lingua:
ENG
Keywords:
CORNELIA DE LANGE SYNDROME; CECAL VOLVULUS;
Tipo documento:
Article
Natura:
Periodico
Settore Disciplinare:
Science Citation Index Expanded
Science Citation Index Expanded
Citazioni:
10
Recensione:
Indirizzi per estratti:
Citazione:
K. Husain et al., "CECAL VOLVULUS IN THE CORNELIA-DE-LANGE-SYNDROME", Journal of pediatric surgery, 29(9), 1994, pp. 1245-1247

Abstract

Cornelia de Lange syndrome is a congenital malformation characterizedby severe growth failure, mental retardation, and multiple physical anomalies. A variety of gastrointestinal anomalies have been described,including malrotation, colonic duplication, and nonfixation of the colon. Two patients with Cornelia de Lange syndrome presented to our institution with acute distal bowel obstruction. In both cases, emergencylaparotomy showed cecal volvulus with necrosis of the terminal ileum,cecum, and ascending colon, secondary to nonfixation of the colon. Resection and an end-ileostomy were performed and later successfully reversed in both patients. Intestinal obstruction is a known cause of death in these children, and nonfixation of the colon has been identifiedduring autopsy. Parents of children with Cornelia de Lange syndrome should be counseled as to the possibility bf bowel obstruction resulting from cecal volvulus. This awareness may lead to earlier identification and treatment of this potentially lethal gastrointestinal tract anomaly. Copyright (C) 1994 by W.B. Saunders Company

ASDD Area Sistemi Dipartimentali e Documentali, Università di Bologna, Catalogo delle riviste ed altri periodici
Documento generato il 07/07/20 alle ore 05:17:16