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Titolo:
LHERMITTE-DUCLOS DISEASE MIMICKING ADULT-ONSET AQUEDUCTAL STENOSIS
Autore:
SIDDIQI SN; FEHLINGS MG;
Indirizzi:
TORONTO HOSP,TORONTO WESTERN DIV,DIV NEUROSURG,399 BATHURST ST,MC 2-435 TORONTO M5T 2S8 ON CANADA TORONTO HOSP,TORONTO WESTERN DIV,DIV NEUROSURG TORONTO M5T 2S8 ON CANADA UNIV TORONTO TORONTO ON CANADA
Titolo Testata:
Journal of neurosurgery
fascicolo: 6, volume: 80, anno: 1994,
pagine: 1095 - 1098
SICI:
0022-3085(1994)80:6<1095:LDMAAS>2.0.ZU;2-F
Fonte:
ISI
Lingua:
ENG
Keywords:
LHERMITTE-DUCLOS DISEASE; DYSPLASTIC GANGLIOCYTOMA; CEREBELLAR VERMIS; AQUEDUCTAL STENOSIS;
Tipo documento:
Note
Natura:
Periodico
Settore Disciplinare:
Science Citation Index Expanded
Science Citation Index Expanded
Citazioni:
7
Recensione:
Indirizzi per estratti:
Citazione:
S.N. Siddiqi e M.G. Fehlings, "LHERMITTE-DUCLOS DISEASE MIMICKING ADULT-ONSET AQUEDUCTAL STENOSIS", Journal of neurosurgery, 80(6), 1994, pp. 1095-1098

Abstract

Lhermitte-Duclos disease is a rare lesion characterized by enlarged cerebellar folia containing abnormal ganglion cells. This case report describes a 51-year-old woman who was initially misdiagnosed as having adult-onset aqueductal stenosis. There were no abnormal findings on computerized tomography (CT), but subsequent magnetic resonance (MR) imaging showed a midline cerebellar lesion extending to the brain stem. This is a unique case of Lhermitte-Duclos disease arising within the cerebellar vermis. The characteristic feature of an enlarged cerebellar hemisphere is absent on CT scans; thus MR imaging is needed to confirmthe diagnosis. If diagnosed late, this generally benign lesion becomes difficult to resect totally and has a poorer prognosis. Only two reports have mentioned the MR imaging characteristics of Lhermitte-Duclosdisease; both described only T-2-weighted images. This case illustrates the full spectrum of MR imaging features of this disease. Both T-1-and T-2-weighted studies showed enlarged cerebellar folia within the lesion. The T-1-weighted image showed a mixed iso- and hypodense signal and the T-2-weighted image a homogeneously increased signal; with gadolinium administration the lesion did not enhance. The latter featuresupports the theory that this disease is a hamartoma rather than a tumor.

ASDD Area Sistemi Dipartimentali e Documentali, Università di Bologna, Catalogo delle riviste ed altri periodici
Documento generato il 02/12/20 alle ore 14:38:31