Catalogo Articoli (Spogli Riviste)

OPAC HELP

Titolo:
KASABACH-MERRITT COAGULOPATHY COMPLICATING KLIPPEL-TRENAUNAY-WEBER-SYNDROME IN PREGNANCY
Autore:
NEUBERT AG; GOLDEN MA; ROSE NC;
Indirizzi:
UNIV PENN,MED CTR,DEPT OBSTET & GYNECOL,DIV MATERNAL FETAL MED,3400 SPRUCE ST PHILADELPHIA PA 19104 UNIV PENN,MED CTR,DEPT OBSTET & GYNECOL,DIV REPROD GENET PHILADELPHIAPA 19104 UNIV PENN,MED CTR,DEPT SURG PHILADELPHIA PA 19104
Titolo Testata:
Obstetrics and gynecology
fascicolo: 5, volume: 85, anno: 1995,
parte:, 2 supplemento:, S
pagine: 831 - 833
SICI:
0029-7844(1995)85:5<831:KCCK>2.0.ZU;2-I
Fonte:
ISI
Lingua:
ENG
Tipo documento:
Note
Natura:
Periodico
Settore Disciplinare:
Science Citation Index Expanded
Citazioni:
8
Recensione:
Indirizzi per estratti:
Citazione:
A.G. Neubert et al., "KASABACH-MERRITT COAGULOPATHY COMPLICATING KLIPPEL-TRENAUNAY-WEBER-SYNDROME IN PREGNANCY", Obstetrics and gynecology, 85(5), 1995, pp. 831-833

Abstract

Background: Klippel-Trenaunay-Weber syndrome is a sporadic genetic syndrome characterized by localized hemangiomas, venous varicosities, and asymmetric osseous hypertrophy of the ipsilateral extremities. Most commonly seen in association with hemangiomas, Kasabach-Merritt syndrome is defined by the presence of thrombocytopenia and a consumptive coagulopathy. Case: A 22-year-old primigravida with a prior diagnosis ofKlippel-Trenaunay-Weber syndrome presented for genetic counseling anddelivery management at 37 weeks' gestation. Large varicosities of thevulva required cesarean delivery. Multiple hemangiomas in the right lower quadrant of the abdomen necessitated the use of a left paramediancutaneous incision. The patient subsequently developed Kasabach-Merritt syndrome and required the transfusion of blood products as well as heparin and aminocaproic acid therapy for her postoperative management. Conclusions: Klippel-Trenaunay-Weber syndrome in pregnancy is rare. The potential for a refractory coagulopathy presenting as Kasabach-Merritt syndrome should be considered in any patient who presents with extensive hemangiomas.

ASDD Area Sistemi Dipartimentali e Documentali, Università di Bologna, Catalogo delle riviste ed altri periodici
Documento generato il 22/10/20 alle ore 12:49:08