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Titolo:
HEMATOLOGICAL DISORDERS AS THE FIRST MANI FESTATIONS OF SARCOIDOSIS WITH HYPOGAMMAGLOBULINEMIA
Autore:
BADERMEUNIER B; FABRE M; GAUTHIER F; TCHERNIA G; CARTRON J; JULLIEN M; DOMMERGUES JP;
Indirizzi:
HOP BICETRE,DEPT PEDIAT,78 RUE GEN LECLERC F-94275 LE KREMLIN BICETR FRANCE HOP BICETRE,SERV ANATOMOPATHOL F-94275 LE KREMLIN BICETR FRANCE HOP BICETRE,HEMATOL LAB F-94275 LE KREMLIN BICETR FRANCE HOP BICETRE,CTR TRANSFUS SANGUINE F-94275 LE KREMLIN BICETR FRANCE CTR HOSP TROYES,SERV PEDIAT F-10003 TROYES FRANCE
Titolo Testata:
Archives de pediatrie
fascicolo: 6, volume: 3, anno: 1996,
pagine: 576 - 579
SICI:
0929-693X(1996)3:6<576:HDATFM>2.0.ZU;2-W
Fonte:
ISI
Lingua:
FRE
Soggetto:
THROMBOCYTOPENIA; SPLENECTOMY;
Keywords:
SARCOIDOSIS; ANEMIA, HEMOLYTIC; THROMBOCYTOPENIA; AGAMMAGLOBULINEMIA; SPLENECTOMY;
Tipo documento:
Article
Natura:
Periodico
Settore Disciplinare:
Science Citation Index Expanded
Citazioni:
17
Recensione:
Indirizzi per estratti:
Citazione:
B. Badermeunier et al., "HEMATOLOGICAL DISORDERS AS THE FIRST MANI FESTATIONS OF SARCOIDOSIS WITH HYPOGAMMAGLOBULINEMIA", Archives de pediatrie, 3(6), 1996, pp. 576-579

Abstract

Background. - Hematological changes are uncommon in childhood sarcoidosis. Case report. - Case 1. This patient developed severe hemolytic anemia associated with splenomegaly at the age of 11 months. A second episode of hemolysis was seen at the age of 6 years; it was associated with thrombocytopenia and hypogammaglobulinemia. A partial splenectomypermitted histological diagnosis of sarcoidosis that was confirmed byelevated angiotensin-converting enzyme level, and subsequently development of pulmonary involvement. Case 2. This boy differed from autoimmune hemolytic anemia and thrombocytopenia associated with splenomegalyat the age of 3 years. At the age of 7 years, he had splenomegaly, enlarged cervical and lomboaortic lymph nodes and hypogammaglobulinemia. Diagnosis of sarcoidosis was made from lymph nodes and spleen biopsies after splenectomy; the patient had increased angiotensin-converting enzyme concentration, and subsequently developed specific renal involvement. Conclusion. - Association of hemolytic anemia, thrombocytopenia, hypogammaglobulinemia and splenomegaly should suggest the diagnosis of sarcoidosis and could be considered as part of the disease spectrum.

ASDD Area Sistemi Dipartimentali e Documentali, Università di Bologna, Catalogo delle riviste ed altri periodici
Documento generato il 01/12/20 alle ore 15:14:19